“…Due to the rarity of this disease and the clinical presentation, it is often misdiagnosed as condyloma acuminata, Bartholin duct cysts, lipoma, vulvar abscess, Gartner duct cyst, vaginal cyst, vaginal prolapse, levator hernia, or sarcoma. Fibroepithelial stromal polyp, superficial angiomyxoma, angiomyofibroblastoma, cellular angiofibroma, and smooth muscle tumors also need to be considered in the differential diagnoses of a polypoidal mass in the perineum [10]. The pathogenesis of this disease is still unclear.…”