Adult Stillʼs Disease

Pouchot, J.; Sampalis, John S.; Beaudet, F; Carette, Simon; DÉCARY, FRANCINE; SALUSINSKY-STERNBACH, MARION; Hill, R.; Gutkowski, Andrzej; Harth, Manfred; Myhal, D; Senécal, Jean‐Luc; Yeadon, C; Esdaile, John M.

doi:10.1097/00005792-199103000-00004

Cited by 533 publications

(125 citation statements)

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“…10 Bir çalışmada, hastaların %34'ü remisyonla, %24'ü intermittant seyretmiş, ancak %36'sında kronik hastalık gözlenmiştir. 11 Olgularımızın taburculuk sonrası klinik takibinde komplikasyona rastlanmamıştır.…”

Section: Olguunclassified

Adult Still disease diagnosed by fever of unknown orgin: Our three-year experiences

Yahyaoğlu¹,

Yilmaz²,

Yazıcı³

et al. 2013

Sakarya Med J

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Section: Olguunclassified

Adult Still disease diagnosed by fever of unknown orgin: Our three-year experiences

Yahyaoğlu¹,

Yilmaz²,

Yazıcı³

et al. 2013

Sakarya Med J

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“…Die Ätiologie ist unklar. Das klinische Bild ist charakterisiert durch eine Trias aus Fieber, flüchtigem Exanthem und Arthritiden (7,8,11), der häufig eine aseptische, nichtexsudative Pharyngitis vorausgeht. Das Fieber tritt meist plötzlich abends oder in der Nacht mit Schüttelfrost auf und normalisiert sich rasch.…”

Section: Diskussionunclassified

“…Destruierende Gelenkveränderungen werden bei chronischem Krankheitsverlauf häufig gesehen. Die Patienten berichten oft über Bauchschmerzen, die bisweilen als "akutes Abdomen" gedeutet werden (8). Laborche- (8), die im Übrigen alle mit einer Therapie mit nicht-steroidalen Antirheumatika assoziiert waren.…”

Section: Diskussionunclassified

“…Kommt es unter Steroidtherapie nicht zu einer Remission, ist die Gabe eines Immunsuppressivums, wie im vorliegenden Fall, zu diskutieren. Substanzen wie Chloroquin, Azathioprin, Cyclophosphamid, Cyclosporin, Sulfasalazin und Immunglobuline wurden mit wechselndem Erfolg eingesetzt (8). Ein neues, vielversprechendes Konzept ist die Therapie mit Tumornekrosefaktor-Inhibitoren, wie z.…”

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Disseminierte intravasale Gerinnung, Perimyokarditis und bilaterales Pleuraempyem bei adultem Still-Syndrom

Krzossok¹,

Benck²,

Woude³

et al. 2004

Dtsch med Wochenschr

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“…While there are several sets of clinical criteria for the classification of AOSD, those of Yamaguchi are used most widely and consist of fever, arthralgia, typical rash, and leukocytosis as major criteria, and sore throat, lymphadenopathy or splenomegaly, liver dysfunction, and the absence of rheumatoid factor (RF) and antinuclear antibody (ANA) as minor criteria [7]. Some manifestations are related to an unfavorable outcome after a chronic disease course and a prolonged period of time until clinical remission, such as typical rash, root joint arthritis, and polyarthritis [8]. …”

Section: Introductionmentioning

confidence: 99%

Application of the international league against rheumatism classification criteria for systemic juvenile idiopathic arthritis as a prognostic factor in patients with adults-onset Still’s disease

et al. 2018

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BackgroundAdult-onset Still’s disease (AOSD) is an adult form of systemic juvenile idiopathic arthritis (JIA) that differs from the latter in its classification. This study evaluated the concordance between the International League Against Rheumatism (ILAR) criteria for systemic JIA and the Yamaguchi criteria and then compared their possible prognostic value in patients with AOSD.MethodsIn a retrospective review of 169 adults with suspected AOSD, patients were classified according to the Yamaguchi or ILAR criteria. Then the concordance in cross-referencing the other group with the different criteria was investigated and the sensitivity and specificity of each set of criteria were determined. Disease activity markers in AOSD patients were correlated with positivity according to both systems.ResultsConcordance was good in patients with suspected AOSD (k = 0.7144, p < 0.001) and low in those with a diagnosis of AOSD (k = 0.3787, p < 0.001). The sensitivity of the ILAR criteria in AOSD patients was 0.8864 (95% confidence interval (CI): 0.8322–0.9405), and the specificity was 0.7838 (0.6511, 0.9164). Positivity according to the ILAR criteria correlated with the systemic score (r = 0.763, p < 0.0001) and C-reactive protein levels (r = 0.183, p = 0.0356) and was associated with a relapse (odds ratio: 1.589, 95% CI: 1.043–2.421), macrophage activation syndrome (MAS; odds ratio: 1.993, 95% CI: 1.218–3.263) and care in the intensive care unit (ICU; odds ratio: 2.087, 95% CI: 1.086–4.011).ConclusionsIn AOSD patients, there is fair concordance between the Yamaguchi and ILAR criteria for systemic JIA. Positive ILAR criteria may be useful for identifying AOSD patients at high risk for relapse, MAS and the need for ICU care. Further studies including larger populations from several centers are needed to confirm our results regarding the utility of the ILAR criteria in AOSD patients.

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Adult Stillʼs Disease

Cited by 533 publications

References 0 publications

Adult Still disease diagnosed by fever of unknown orgin: Our three-year experiences

Adult Still disease diagnosed by fever of unknown orgin: Our three-year experiences

Disseminierte intravasale Gerinnung, Perimyokarditis und bilaterales Pleuraempyem bei adultem Still-Syndrom

Application of the international league against rheumatism classification criteria for systemic juvenile idiopathic arthritis as a prognostic factor in patients with adults-onset Still’s disease

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