Acute Occlusion of Left Coronary Ostium Associated With Congenital Quadricuspid Aortic Valve

Mutsuga, Masato; Tamaki, Shuji; Yokoyama, Yoshiro; Kato, Noriyuki; Yokote, June; Ohata, Norihisa

doi:10.1016/j.athoracsur.2003.11.052

Cited by 12 publications

(10 citation statements)

References 5 publications

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“…The association of QAV and single coronary ostium is very rare and has only been reported in one case before [1]. This association is of importance as there has been a report of sudden cardiac death due to a dome-like occlusion of the left main coronary ostium by the accessory cusp [29] and acute myocardial infarction in another patient from partially adhered small aortic cusp to the orifice of the left main coronary artery [30].…”

Section: Reported Cardiac and Systemic Associations With Qavsmentioning

confidence: 99%

Quadricuspid Aortic Valve, Single Coronary Artery, Solitary Kidney and Oblique Facial Cleft. A Unique Constellation of Congenital Abnormalities: Case Report and Review of the Literature

Mehisen¹,

Essely²

2016

J Genet Syndr Gene Ther

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Quadricuspid aortic valve (QAV) is a rare congenital anomaly which is associated with coronary artery anomalies in 10% of the patients. The association of QAV with single coronary artery (SCA) is very rare has been reported only in one case previously. We report the case of a 30-year-old male patient with a unique constellation of congenital anomalies including QAV, SCA, solitary kidney and Tessier type 3 oblique facial cleft with cleft palate. To our knowledge, this unique combination has never been described previously. We describe his case and review the topic of QAV and its reported cardiac and systemic associations.

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Section: Reported Cardiac and Systemic Associations With Qavsmentioning

confidence: 99%

Quadricuspid Aortic Valve, Single Coronary Artery, Solitary Kidney and Oblique Facial Cleft. A Unique Constellation of Congenital Abnormalities: Case Report and Review of the Literature

Mehisen¹,

Essely²

2016

J Genet Syndr Gene Ther

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“…In addition, histology revealed disarrangement of the elastin fibres typical of supravalvar aortic stenosis. Isolation of the left coronary artery by 1 leaflet adherent to the aortic wall was also diagnosed in a girl aged 10 year during an emergency operation for an acute myocardial infarction 14 . The anomaly was also found during surgery for coronary arterial orificial atresia in a 5 year old child affected by supravalvar aortic stenosis 15 .…”

Section: Discussionmentioning

confidence: 95%

“…Isolation of the left coronary artery by 1 leaflet adherent to the aortic wall was also diagnosed in a girl aged 10 year during an emergency operation for an acute myocardial infarction. 14 The anomaly was also found during surgery for coronary arterial orificial atresia in a 5 year old child affected by supravalvar aortic stenosis. 15 In all our patients, the coronary arteries arose in their expected fashion from the aortic sinuses adjacent to the pulmonary trunk.…”

mentioning

confidence: 91%

Congenital quadricuspid aortic valve in children

et al. 2008

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Quadricuspid aortic valves are rare congenital anomalies, usually diagnosed in adult patients affected by severe aortic regurgitation. We have now encountered three such valves in children undergoing transthoracic echocardiography. All children were asymptomatic. The first child possessed a valve with two larger leaflets, and smaller leaflets of equal size. In the second child, 3 leaflets were of equal size, with 1 small accessory leaflet. The third child had a valve with four leaflets of approximately equal size. In one child, the aortic valve was functioning normally, and came to attention because of mitral valvar prolapse causing mild regurgitation. In the remaining two children, central mild aortic regurgitation was detected using colour flow analysis, and associated dilation of the aortic root was revealed by measurements of the cross-sectional images.

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“…Důsledkem protrahované ischemie myokardu může být i vznik akutního infarktu myokardu již v dětském věku nebo v období dospívání. 5,6 Jindy se anomálie může manifestovat jako akutní levostranná srdeční insufi cience nebo vede ke vzniku maligní arytmie s následkem úmrtí. Proto uzávěr ústí věnčité tepny cípem aortální chlopně představuje závažný rizikový faktor náhlé srdeční smrti.…”

Section: Kasuistiky | Case Reportsunclassified

Closure of the left coronary artery orifice by a cusp of quadricuspid aortic valve with aortic insufficiency

Pečenková¹,

Marek²,

Karmazin³

et al. 2011

Cor Vasa

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Čtyřcípá aortální chlopeň je vzácnou vrozenou anomálií, která byla poprvé popsána v roce 1862. Autoři uvádějí případ 58letého muže s nálezem insufi cientní čtyřcípé aortální chlopně, uzávěrem ústí levé věnčité tepny jedním z jejích cípů a anomálním zásobením srdečního svalu pomocí kolaterálního řečiště s průkazem přetrvávající námahové ischemie myokardu, který se u pacienta manifestoval levostrannou kardiální dekompenzací. Klíčová slova: Čtyřcípá aortální chlopeň-Aortální regurgitace-Anomálie věnčitých tepen Pečenková V, Marek T, Karmazín V, et al. Closure of the left coronary artery orifi ce by a cusp of quadricuspid aortic valve with aortic insuffi ciency.

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Acute Occlusion of Left Coronary Ostium Associated With Congenital Quadricuspid Aortic Valve

Cited by 12 publications

References 5 publications

Quadricuspid Aortic Valve, Single Coronary Artery, Solitary Kidney and Oblique Facial Cleft. A Unique Constellation of Congenital Abnormalities: Case Report and Review of the Literature

Quadricuspid Aortic Valve, Single Coronary Artery, Solitary Kidney and Oblique Facial Cleft. A Unique Constellation of Congenital Abnormalities: Case Report and Review of the Literature

Congenital quadricuspid aortic valve in children

Closure of the left coronary artery orifice by a cusp of quadricuspid aortic valve with aortic insufficiency

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