“…The presence of other body tissues like penis, bladder, skin appendage, presacral mass, bowel tissue, etc., coexisting with the accessory limb, support this theory [8,9,10]. Others believe that faulty secondary neurulation causes this defect [2,11,12]. Oversecretion of neural tube fluid during faulty neurulation collects under the skin and manifests later as a differentiated accessory limb.…”