AB0587 Limitations of the 1990 American College of Rheumatology Criteria in the Classification of Cutaneous Vasculitis. Study of 773 Cutaneous Vasculitis

Abstract

Background In 1990 The American College of Rheumatology (ACR) established criteria for the classification of vasculitis. Cutaneous vasculitis (CV) comprises a wide and heterogeneous group of entities. Objectives Our aim was to revise the usefulness of ACR-1990 criteria in classifying patients with CV. Methods Retrospective study of a wide and unselected series of patients with CV from a single university hospital from January 1976 to January 2012. Patients were classified according to the 1990 ACR methodology and criteria. Results 773 Patients (351 women/422 men) with a mean age of 34.1±27.4 years were diagnosed as having CV. Applying the 1990 ACR criteria patients were classified as secondary to connective tissue diseases (n=35), major infections (n=27), malignancies (n=16), mixed essential cryoglobulinemia (n=13), Wegener Granulomatosis (n=3), Churg-Strauss syndrome (n=3) and Polyarteritis nodosa (n=3). The remaining 673 patients were classified as Hipersensitivity vasculitis (n=247; 36.6%) or Henoch Schönlein Purpura (n=414; 61.4%). Disappointingly, 127 (18.8%) met criteria for both entities and 12 out of 673 cases did not meet criteria for HV nor HSP and were not classified. Conclusions The ACR-1990 criteria for vasculitis do not properly classify patients with CV. Acknowledgements This study was supported by a grant from “Fondo de Investigaciones Sanitarias” PI12/00193 (Spain). This work was also partially supported by RETICS Programs, RD08/0075 (RIER) and RD12/0009/0013 from “Instituto de Salud Carlos III” (ISCIII) (Spain). Disclosure of Interest None declared DOI 10.1136/annrheumdis-2014-eular.3111