Background: Human tails are rare entities and can be classified as true tails and pseudotails. True tails are composed of adipose tissue, connective tissue, muscles, vessels, nerves, and mechanoreceptors whereas pseudotails may be an anomalous prolongation of the coccygeal vertebra, lipoma, teratoma, chondrodystrophy or parasitic fetus. Case Presentation: A 3-month-old male baby had a tail like appendage since birth which was gradually increasing in size. After complete workup, an elective resection was done under general anesthesia. Postoperative recovery was uneventful. Conclusion: Surgical excision of the tail is the ultimate and may be the only surgical intervention required in these patients.