A Rare Paraspinal Desmoid Tumour following Instrumented Scoliosis Correction in an Adolescent

McCabe, Fergus J.; Hussey, Alan; McCabe, John P.

doi:10.1155/2021/6665330

Cited by 1 publication

(2 citation statements)

References 24 publications

(39 reference statements)

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“…2,4 The tumor's slow growing, benign course in our case is typical of desmoid tumor. 9,15,19,37,38 The gradual compression of the spinal cord produced increasing numbness, weakness, paresthesia, and abnormal gait, all consistent with published reports of paraspinal desmoid tumor. The present case is unique not only because of the tumor's rare paraspinal location, but also because most previously reported para-spinal desmoid tumor patients had previous surgery or trauma in the area of the tumor.…”

Section: Discussionsupporting

confidence: 88%

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Paraspinal Desmoid Tumor in a Pediatric Patient with No Surgical History: A Case Report

Patel,

Varga,

Mallela

et al. 2024

Asian J Neurosurg

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Desmoid tumors are locally aggressive, benign neoplasms originating in connective tissues. Although the exact pathophysiology remains unknown, antecedent trauma or surgery are believed to be important contributing factors. The occurrence of paraspinal desmoid tumor in pediatric patients is extremely uncommon. Here, we present an exceedingly rare case of a pediatric patient with no surgical or family history who developed a paraspinal desmoid tumor.A 9-year-old female patient presented with 4 months of progressive back pain, right lower extremity weakness, and numbness. Spinal imaging revealed a left epidural paraspinal mass compressing her thoracic spinal cord and extending into the left thoracic cavity. A multidisciplinary approach with neurosurgery and thoracic surgery enabled gross total resection of the lesion. The patient had complete resolution of her symptoms with no signs of residual tumor on postoperative imaging. Pathology revealed a desmoid tumor that avidly stained for beta-catenin. On her last follow-up, she developed a recurrence, to which she was started on sorafenib therapy.Desmoid tumors are rare connective tissue neoplasms that often occur after local tissue trauma, such as that caused by surgery. This report presents a rare case of a pediatric paraspinal desmoid tumor that occurred in a patient with no surgical or family history. Such tumors should undergo surgical resection for symptomatic relief and tissue diagnosis. Close clinical and radiographic surveillance are essential in these patients due to the high recurrence rates of desmoid tumor.

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Section: Discussionsupporting

confidence: 88%

“…To the best of our knowledge, there are only 7 reported cases of paraspinal desmoids in pediatric patients. [10][11][12][13][14][15][16] Here, we present a rare case of a pediatric extradural paraspinal desmoid tumor in a patient with no prior surgical or familial history.…”

Section: Introductionmentioning

confidence: 99%