A rare giant scalp dermatofibrosarcoma protuberans

Arifin, Muhammad Zafrullah; Yudoyono, Farid; Dahlan, Rully Hanafi; Hernowo, Bethy S.; Sutiono, Agung Budi; Faried, Ahmad

doi:10.4103/2152-7806.129909

Cited by 4 publications

(4 citation statements)

References 11 publications

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“…[2] History revealed that the DFSP recurred in the second year after the first tumor excision [Figure 1c]. On physical examination, there was a irregular, skin-colored, multiple lobulated mass, measuring 12 × 10 × 5 cm in diameter, with a fixated base; head computed tomography (CT) shown no intracranial mass [Figure 1d].…”

Section: Case Reportsmentioning

confidence: 99%

“…We present a case of a 29-year-old adult male whose main complaint was a recurrent lump, a painless lesion, on his mid frontal region after tumor excision who was diagnosed with DFSP 4 years ago [Figure 1a and b ]. [ 2 ] History revealed that the DFSP recurred in the second year after the first tumor excision [ Figure 1c ]. On physical examination, there was a irregular, skin-colored, multiple lobulated mass, measuring 12 × 10 × 5 cm in diameter, with a fixated base; head computed tomography (CT) shown no intracranial mass [ Figure 1d ].…”

Section: Case Reportsmentioning

confidence: 99%

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Recurrence case of rare scalp dermatofibrosarcoma protuberans: Two case reports of a wide radical excision, craniectomy bone involvement followed by cranioplasty and reconstruction

2017

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Background:Dermatofibrosarcoma protuberans (DFSP) is a rare low-grade sarcoma of the fibroblast originating from the dermal layer of the skin, characterized by a locally aggressive growth and high rate of local recurrence.Case Description:Two patients underwent a wide radical excision of recurrent scalp DFSP which was reconstructed with translational skin flap and split-thickness skin graft. We described above cases several years ago with a local excision of the tumor; recently, they developed local recurrence of DFSP with calvarial involvement. We then performed a wide radical excision, with craniectomy of the cranial defect followed by cranioplasty using titanium mesh, continuing with reconstruction.Conclusion:A successful treatment and management depends on achieving local control and preventing cosmetic and functional deficit; all efforts should be made for complete excision. Postoperative follow-up recommended for highly suspicious cases and annual checkups should be performed up to 5 years after definitive therapy.

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Section: Case Reportsmentioning

confidence: 99%

Section: Case Reportsmentioning

confidence: 99%

Recurrence case of rare scalp dermatofibrosarcoma protuberans: Two case reports of a wide radical excision, craniectomy bone involvement followed by cranioplasty and reconstruction

2017

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“…These lesions are often located on the trunk and extremities; however, dermatofibrosarcoma has been reported in many other areas such as scalp, breast, pubic area, and vulva. [ 6 7 8 9 10 11 ] Therefore, the presentation also depends on area involved. It can present as mass in the scalp, breast or vulva, and extremities.…”

Section: Clinical Presentationmentioning

confidence: 99%

Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor

Barwani

Taif

Mazrouai

et al. 2016

Journal of Clinical Imaging Science

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Dermatofibrosarcoma protuberans (DFSP) is a rare soft tumor which originally represents a cutaneous sarcoma. It grows slowly and presents usually as nodular superficial lesion on the trunk or the extremities. Although these tumors are locally aggressive with high rate of recurrence following surgery; the prognosis is considered excellent when it is effectively treated. The radiological appearance of this tumor has rarely been studied and findings infrequently discussed in the literature probably because many lesions underwent resection before imaging. Although imaging is infrequently performed for this lesion; it can show characteristic features and demonstrate the full extent. Imaging may also play a role in the differentiation of this tumor from more serious soft tissue lesions such as more aggressive sarcomas and hemangioma. In this article, we discuss the imaging findings of DFSP that can aid in its diagnosis and its variable appearances. In addition; the clinical presentation and treatment options are also described with review of the previous literature.

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“…[ 8 ] Clinically, it may be confused with other conditions such as sclerosing basal cell carcinoma, morphea, scar, and anetoderma. [ 8 9 ] On histopathology, it shows spindle-shaped neoplastic cells arranged in cartwheel or storiform pattern in the dermis. [ 7 ] Immunohistochemical stains are employed to differentiate DFSP from dermatofibroma, as sometimes it is difficult to differentiate the two on routine H and E stain.…”

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confidence: 99%