Epidermoid cysts are developmental lesions and may be seen in the head and neck area with an incidence rate of 2% as well as in different organs of the body. Epidermoid cysts are located in sublingual, submental, submandibular and buccal mucosa and rarely at tonsils in the head and neck area. They congenitally occur in fetal period or occur as an acquired lesion due to a trauma or implant after surgery. In this case report, we will discuss the epidermoid cyst, a rare incidental finding developing at tonsils, in a 6-year-old boy with chronic tonsillitis with literature review. In conclusion, tonsil hyperplasia may also be caused by cystic developments at the tonsils. It should clinically be kept in mind especially in differential diagnosis of malignancy in the asymmetry of tonsils. All tonsillectomy materials should be detailed examined gross and histopathologically for additional pathologies that may be found in addition to tonsillitis and reactive lymphoid hyperplasia.