A Rare Case of Herlyn Werner Wunderlich Syndrome (HWWS) with Urethrovaginal Fistula

Abstract

Herlyn Werner Wunderlich Syndrome (HWW) is a rare congenital malformation of female urogenital tracts. We report our first case of HWWS with urethrovaginal fistula in Lady Aitchison Hospital Lahore. A 27 years old lady presented with hematuria and urinary retention having single opening at vulva with menstrual blood and urine draining through it. Examination under anesthesia showed uretheral opening in anterior wall of lower 1/3 of vagina.MRI showed uterus didelphus with two cervices and vagina (atresia of lower 2/3 on left side) and absent left kidney.Surginal treatment by creating a separate opening of neourethra was made by Urology Department of Mayo Hospital. Keywords: Herlyn Werner Wunderlich syndrome, urethrovaginal fistula, urogenital tract

Unusual clinical presentations, pathogenesis and radiological review of Herlin-Werner-Wunderlich syndrome: A case report and literature review

“…“A Rare Case of Herlyn Werner Wunderlich Syndrome with Urethrovaginal Fistula” is the title of a case reported by Meher-un-Nisa et al., in which a 27-year-old lady presented with hematuria and urinary retention was diagnosed with HWW syndrome. The patient had only a single opening in the vulva through which urine and menstrual flow were drained [24] .…”