A Rare Case of Double-System With Ectopic Ureteral Openings Into Vagina

Duicu, Carmen; Kiss, Éva; Simu, Iunius; Aldea, Cornel

doi:10.3389/fped.2018.00176

Cited by 21 publications

(25 citation statements)

References 13 publications

Supporting

Mentioning

Contrasting

Unclassified

Order By: Relevance

“…Urinary tract abnormalities require multidisciplinary approach regarding the diagnosis, treatment and prognosis. [6,7,8] PBS can be a life threatening disease, especially when the urethral atresia is not compensated by a patent urachus, thus leading to oligohydramnios and pulmonary hypoplasia [3] . The latter variant is the most severe (grade 1).…”

Section: Discussionmentioning

confidence: 99%

Long term follow-up in a patient with prune-belly syndrome – a care compliant case report

Aldea¹,

Duicu

Delean³

et al. 2019

Medicine

Self Cite

View full text Add to dashboard Cite

Rationale:Malformative uropathies represent a major cause of Chronic Kidney Disease (CKD) in children. Genitourinary system is the most frequent and sever affected in Prune-Belly syndrome cases. That is why the findings of early diagnosis and vigilant monitoring for these situations remain a major challenge for the medical team.Patient concerns:We present the clinical course of a 10 years old child with diagnosis of Prune-Belly syndrome. A urinary tract abnormality was suspected starting 25 weeks of gestation, when a routine ultrasound showed oligohydramnios, increased size urinary bladder, bilateral hydronephrosis and megaureters, thin abdominal wall.Diagnosis:Prenatal suspicion of Prune-Belly syndrome plays a deciding role in renal disease progression. A detailed clinical exam at birth established the diagnosis of Prune-Belly syndrome. Renal ultrasound confirmed bilateral grade III hydronephrosis and megaureters, with empty bladder, suggesting an obstruction at this level. A persistent urachus was confirmed by catheterization. Later it was used for imaging study that showed bilateral high grade reflux.Interventions:The main goal of any treatment is to preserve kidney function. Treatment options depend on the clinical picture. The pregnancy was closely monitorized, but fetal distress appeared so early labor was induced at 32 weeks. At beginning a temporary catheter was placed into the urachus which expressed urine. The urachus drain was left in place until the age of 6 weeks, when a bilateral ureterostomy was performed. Skeletal and genital malformations were present too; the child has undergone several surgeries to solve these abnormalities.Outcomes:At the age of 10 years, he is a well-adapted child. He has had fewer than 3 urinary tract infections per year. Long term follow-up showed a relatively slow decline in the estimated Glomerular Filtration Rate in our child (62 ml/1.73m2/min).Lessons:This case suggests that induced early labor could prove beneficial for early upper urinary tract decompression through earlier access to surgery. This is an option especially in situations or region where vesicoureteric or vesicoamniotic shunt placement is not available.

show abstract

Section: Discussionmentioning

confidence: 99%

Long term follow-up in a patient with prune-belly syndrome – a care compliant case report

Aldea¹,

Duicu

Delean³

et al. 2019

Medicine

Self Cite

View full text Add to dashboard Cite

show abstract

“…Alternatively, Stephen's ectopic pathway postulates that Weigert-Meyer's law may be broken. 2 Instead of the ectopic ureter draining inferomedially to the orthotopic ureteric orifice location, rarely it may drain superomedially to it.…”

Section: Descriptionmentioning

confidence: 99%

Rupture of a massive hydronephrotic upper pole moiety: a sequalae of mild trauma

et al. 2020

View full text Add to dashboard Cite

“…Pilihan teknik pembedahan lain adalah nefro-ureterektomi/heminefro-ureterektomi bila fungsi ginjal sudah buruk. 6,7 Berkaitan dengan pemaparan di atas, maka laporan kasus ini bertujuan untuk mengevaluasi kasus sistem tunggal ureter ektopik dengan ginjal multikistik displastik di RSUP Sanglah, Bali, Indonesia maupun tata laksana terkini luaran klinis pasca tindakan operasi yang telah dilakukan.…”

Section: Abstrakunclassified

Sistem tunggal ureter ektopik dengan ginjal multikistik displastik di RSUP Sanglah, Bali, Indonesia: laporan kasus

Oktavius¹,

Duarsa²

2020

Intisari Sains Medis

View full text Add to dashboard Cite

Background:Â Ectopic ureter is a condition when the ureter does not enter the bladder properly. The occurrence of the ectopic ureter is 1:2.000 - 1:4.000 in general population with gender ratio 6:1 in favour of females. More than 80% of cases of ectopic ureters are generally associated with complete duplication of the pelvic-ureteric system. Still, the ectopic ureter can also occur in a single pelvic-ureteric system, which is typically dysplastic or poorly functioning, such as in multicystic dysplastic kidney. This study aims to evaluate the current management of a single ectopic ureteral system with dysplastic multicystic kidneys at Sanglah General Hospital, Bali, Indonesia.Case Description:Â A 3-year-old girl was referred to the urology clinic of Sanglah General Hospital with chief complaint cloudy urinary since 1,5 years ago. Past medical history, the patient had a recurrent urinary tract infection with fever. Physical examination and laboratory findings were normal. However, an abdominal ultrasound showed a multicystic dysplastic kidney. VCUG showed vesicoureteral reflux grade V and ectopic ureter. Cystoscopy with retrograde pyelography and ureterorenoscopy showed an ectopic ureter opening was located in the proximal urethra above the external sphincter. Nephroureterectomy was performed. After the surgical procedure, the patient was treated and had no complaint. The patient was discharged from the hospital four days after surgery.Â Conclusion:Â The management of ectopic ureteral cases varies for each case. In this regard, the nephroureterectomy surgery performed in the case has provided good outcomes.Latar Belakang: Ureter ektopik merupakan suatu kondisi dimana ureter tidak masuk ke buli-buli pada tempat yang seharusnya. Insiden ureter ektopik 1:2.000 - 1:4.000 kelahiran pada populasi secara umum dengan perbandingan jenis kelamin perempuan lebih banyak daripada laki-laki, yaitu 6:1. Lebih dari 80% kasus ureter ektopik umumnya berhubungan dengan duplikasi sistem pelvis-ureter yang lengkap. Tetapi ureter ektopik juga dapat terjadi pada sistem pelvis-ureter tunggal, yang pada umumnya displastik atau fungsinya buruk, seperti pada keadaan ginjal multikistik displastik. Studi ini bertujuan untuk mengevaluasi manajemen terkini pada sistem tunggal ureter ektopik dengan ginjal multikistik displastik di RSUP Sanglah, Bali, Indonesia.Deskripsi Kasus: Seorang anak perempuan berusia 3 tahun dirujuk ke poliklinik urologi Rumah Sakit Sanglah dengan keluhan buang air kecil keruh sejak 1,5 tahun lalu. Riwayat penyakit dahulu, penderita mengalami infeksi saluran kemih berulang disertai demam. Hasil pemeriksaan fisik dan laboratorium normal. Hasil USG abdomen menunjukkan gambaran ginjal multikistik displastik, VCUG menunjukkan vesikoureteral refluks grade V dan ureter ektopik. Sistoskopi dengan retrograde pyelografi dan ureterorenoskopi menunjukkan muara ureter ektopik terletak di uretra proksimal di atas sfingter uretra eksterna. Lalu dilakukan tindakan nefroureterektomi. Setelah dioperasi, selama perawatan, pasien tidak memiliki keluhan. Pasien dipulangkan setelah empat hari perawatan.Kesimpulan: Tatalaksana pada kasus ureter ektopik bervariasi untuk setiap kasus. Berkaitan dengan hal tersebut maka tindakan pembedahan nefrouretektomi yangÂ dilakukan pada kasus tersebut telah memberikan luaran yang baik.

show abstract

A Rare Case of Double-System With Ectopic Ureteral Openings Into Vagina

Cited by 21 publications

References 13 publications

Long term follow-up in a patient with prune-belly syndrome – a care compliant case report

Long term follow-up in a patient with prune-belly syndrome – a care compliant case report

Rupture of a massive hydronephrotic upper pole moiety: a sequalae of mild trauma

Sistem tunggal ureter ektopik dengan ginjal multikistik displastik di RSUP Sanglah, Bali, Indonesia: laporan kasus

Contact Info

Product

Resources

About