A Rare and Atypical Mullerian Anomaly With Duplication and Agenesis Without Any Present Classification

Abstract

A 29 year old unmarried woman with primary amenorrhea consulted her doctor. On further questioning the patient complained of monthly cyclical severe pain abdomen for 2-3 days which was relieved only after administration of injectable pain killers like tramadol. She also gave history of vaginoplasty done 8 years back. On examination the patient was of thin built and her secondary sexual characters were well developed. Her per abdominal examination was normal. On per vaginal examination cervix and uterus was not felt and vaginal length was 3 cm. On per rectal examination also uterus was not felt. She was sent for ultrasound examination that showed two separate uteri with fundus and body but no cervix, both ovaries were present. After routine work up and investigations patient was put up for laparotomy, right sided hysterectomy with salpingooophorectomy and left sided hysterectomy with removal of fallopian tube done while left ovary was preserved. Thus, a rarest anomaly of mullerian system was reveled and managed leading to freedom of patient of her monthly cyclical severe abdominal pain.