A new syndrome of multiple hemangiomas, right dominant double aortic arch, and coarctation

Abstract

Brief communications 1207 ble aortic arch, type B interruption of the left arch, coarctation, aberrant subclavian arteries, and associated multiple right-sided facial and upper limb superficial and deep hemangiomas.Clinical summaries PATIENT 1. A baby girl was born by elective cesarean birth for cephalopelvic disproportion at term in August 1984 and required ventilatory assistance for 6 days for hyaline membrane disease. During this period she was found to have a continuous cardiac murmur and heart failure. There was no history of congenital heart disease in the family, which included one healthy sibling. Multiple capillary hemangiomas were noted over the right side of her face, shoulder, and arm and a deeper hemangioma was present on the back of her neck.Congenital aortic lesions are occasionally associated with clinical syndromes. Recognition of these syndromes is important in aiding clinical diagnosis and accurate surgical management. We describe the case histories of 2 children who appear to have a new vascular syndrome comprising right dominant dou-

Right Aortic Arch and Coarctation: A Rare Association

“…The cases described in this report are consistent with previous reports 3,9 , 12 that included other congenital heart abnormalities along with the abnormal aortic arch architecture except that our study showed a higher frequency of congenital heart defects. Although the numbers are relatively small, our series was much larger than any of those previously reported…”

“…Two had heterotaxy syndrome, 2 had Goldenhar syndrome, and 1 had DiGeorge syndrome. One of our patients (patient 7) had a scalp hemangioma, which was at least evocative of a recent report by Wong and associates, 12 which reported 2 patients with similar arch anomalies to our patient and multiple hemangiomas.…”

“…A more recent review of cases of right aortic arch associated with vascular obstruction noted a number of cases in the literature; 3 however, all of those with coarctation were single‐case reports, save 1 with 2 cases 8 . More recent reports have also consisted of descriptions of 1 or 2 cases, occasionally in association with other anomalies or syndromes 9–12 . Finally, an ideal surgical approach for these patients has been defined through only a small number of cases 13 …”

“…8 More recent reports have also consisted of descriptions of 1 or 2 cases, occasionally in association with other anomalies or syndromes. [9][10][11][12] Finally, an ideal surgical approach for these patients has been defined through only a small number of cases. 13 We undertook the present study to review our institutional experience in this disorder.…”

Double Aortic Arch with Coarctation of Aorta in an Adolescent: Unraveling the Vascular Ring

“…2 Numerous variations can be seen, including of COA and vascular ring, with double aortic arch (DAA) being the most common anomaly, frequently causing compression of the trachea and/or esophagus. [2][3][4] We present such a case that underwent successful surgical correction.…”