A New Minimally Invasive Aesthetic Procedure for Correction of Frontal Coup de Sabre Deformity in Romberg’s Syndrome

Agrawal, Kapil; Desai, Vyoma; Choudhary, Sushant; Vora, Sameer; Gupta, Shikha; Bachhav, Manoj

doi:10.1007/s12663-014-0646-4

Cited by 6 publications

(4 citation statements)

References 27 publications

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“…Agrawal and colleagues 28 reported a patient who previously underwent autologous fat grafting for an ECDS lesion with underlying bone involvement. The authors observed reversibility of the achieved aesthetic result and decided that a second procedure is necessary.…”

Section: Discussionmentioning

confidence: 99%

Management Options for Linear Scleroderma (“En Coup de Sabre”)

2022

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BACKGROUND En coup de sabre (ECDS) is a form of linear-scleroderma, primarily affecting the face. Despite effectiveness of pharmacological interventions in the management of lesions, sequelae of cutaneous deformities are common. OBJECTIVE Review the existing surgical tools for the correction of "en coup de sabre" ECDS lesions and facial deformities. MATERIALS AND MethodsThe authors conducted a literature search for reports on surgical interventions for ECDS deformations, in the electronic databases of PubMed, Scopus, and Cochrane Library Databases. RESULTS Twenty-six publications reporting 39 patients were found in the literature. The average age of patients was 25 6 4.7 years. Thirty-one of the patients were females. Six methods were found in the literature for surgical correction of ECDS. Fat grafting was performed in 41% of patients, surgical reconstruction in 18%, injectable fillers in 15%, implants in 10%, botulinum toxin injections in 8%, and bone/cartilage grafts in 8%. Imaging studies of the skull and face were performed in 36% of patients. Bony defects were found in 64.3% of them. CONCLUSION Different surgical and minimally invasive options exist in the armamentarium of clinicians correcting ECDS deformities. Tailoring the method of correction to patient's needs and expectation is crucial in ensuring patient satisfaction.

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Section: Discussionmentioning

confidence: 99%

Management Options for Linear Scleroderma (“En Coup de Sabre”)

2022

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“…Successful treatment with autologous fat grafting was achieved, only to be repeated 6 months later due to significant resorption. 25 Overcorrecting the defect to compensate for the expected fat resorption is one way of addressing the certainty of partial resorption. 26 Another measure to increase fat graft survival at the recipient site includes placing the fat injectate in microdroplets of no more than 0.1 cc per aliquot, as described by Coleman.…”

Section: Discussionmentioning

confidence: 99%

“…Similarly, Agrawal et al described LScs in a 19‐year‐old woman who presented with a depression in the forehead. Successful treatment with autologous fat grafting was achieved, only to be repeated 6 months later due to significant resorption 25 …”

Section: Discussionmentioning

confidence: 99%

Treatment of linear scleroderma “En coup de Sabre” with single‐stage autologous fat grafting: A case report and review of the literature

Ayoub

Saba

2020

J of Cosmetic Dermatology

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Linear scleroderma "en coups de sabre" (LScs) is a variant of localized scleroderma, which is confined to the hemiface but may occasionally be bilateral. 1 First described by Addison in 1854, disease incidence peaks during the fifth decade of life. However, in children, it is often diagnosed between the ages of 2-14 years, and it affects females more than males (3:1). Clinical manifestations include scar-like lesions in the forehead and the scalp, and atrophy of the underlying skin and subcutaneous tissues including muscle, tendon, and bone. 1-5 In the craniofacial region, intracranial neural structures may be involved, with some patients exhibiting seizures. 5 The soft-tissue changes often progress slowly over a period of 2-5 years, after which the disease stabilizes. 6-8 The result is an acute facial asymmetry that can be distressing to the affected young adults. 9,10 Medical treatments in terms of immunosuppressants and anti-inflammatory drugs do not adequately address the soft-tissue atrophy. Thus, surgical correction has continued to be a mainstay of treatment. 2,9,11 It is important to distinguish LScs from Parry-Romberg syndrome, where the latter often initiates in the cheek and nose, is unilateral, and does not exhibit skin changes. 5 In this report, we present a rare case of LScs that was successfully managed by single-stage autologous fat grafting.

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“…5 Although the characteristics that the PHA presents are visible and easily evaluable in its beginnings and due to its slow evolution it is possible to confuse it with different pathologies of similar manifestation, among them the most common, the scleroderma (morphea) in courp de saber (ECDS) that exhibits a marked hemifacial scleroderma that is related in large measure to cases of PHA. [5][6][7][8] Rasmussen's encephalitis is an inflammatory hemiencephalic condition characterized by the appearance of seizures in those who have it in a similar way as can be seen in many individuals with PHA and in the other hand the lipodystrophy that characterizes a Barrequer-Simons syndrome in its beginnings in a localized way in the face can also become confused with the PHA. [9][10][11][12] PHA, appearing during the first two decades of life, commonly alters the correct development of facial bones, so it is possible to confuse it with different facial asymmetries of various syndromes, such as Goldenhar's.…”

Section: Introductionmentioning

confidence: 99%

Individual replacement prosthesis: contemporaneous treatment of parry-Romberg syndrome. A case report

Vergara¹,

Caro²,

Mora

2018

JDSOMR

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Introduction: Parry-Romberg syndrome or progressive hemi facial atrophy is a slow and localized disorder of facial tissues that appears in early and middle age characterized by degeneration of the subcutaneous tissues which affects the symmetry of the face.Case report: 18-year-old male individual who presented facial asymmetry with evidence of alterations in both the intraoral and extraoral volume. Conclusion:In order to get an adequate treatment of the parry-romberg syndrome an interdisciplinary approach is required after an adequate study of the case to execute a treatment supported by a good scientific base, achieved through the use of the design and manufacture of stereolithography.

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A New Minimally Invasive Aesthetic Procedure for Correction of Frontal Coup de Sabre Deformity in Romberg’s Syndrome

Cited by 6 publications

References 27 publications

Management Options for Linear Scleroderma (“En Coup de Sabre”)

Management Options for Linear Scleroderma (“En Coup de Sabre”)

Treatment of linear scleroderma “En coup de Sabre” with single‐stage autologous fat grafting: A case report and review of the literature

Individual replacement prosthesis: contemporaneous treatment of parry-Romberg syndrome. A case report

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