A new case of male Y-type urethral duplication and review of literature

Congenital urethroperineal fistula with scrotal localization: A case report

“…Per this classification, the type II A2 variety refers to complete urethral duplication in which a patient presents with 2 urethral meatuses. A large ventral second channel is observed to originate from a hypoplastic, dorsal orthotopic urethra and when the two channels exit independently, they present a "Y" shaped configuration [5]. Thus, CUFP resembles the Y-type urethral duplication, although both entities clearly differ with respect to their anatomopathologic features [9,10].…”

“…Several names have been used to refer to this pathology: congenital Y-type urethroperineal fistula, Y-type urethral duplication in a male, or Y-type congenital urethral duplication [4,5,7]. A few authors consider CUPF to be a congenital urethral duplication associated with a normal dorsal urethra and a small ventral fistula extending to the perineal skin [7], which could be categorized as a unique form or variation of urethral duplication [1,5,8]. The Effmann's classification describes different types of urethral duplication [7].…”

“…It is usually expected that a fistula would be lined by squamous epithelium [6]. A second argument in favor of this proposition is the absence of factors predisposing to the formation of a fistula (e.g., presence of infection, trauma, or foreign bodies) [5].…”

“…Consequently, there originates an accessory urogenital sinus [2,8]. Pressure atrophy from the heel of the fetal foot and a vascular accident have been viewed as possible etiologies of the anomalies [5,14]. The urethral opening of the fistula is located within the prostatic urethra, usually near the verumontanum or close to the bladder neck [1,[3][4][5][6][7][8][9][10][11][12][13][14].…”

“…Most patients clinically present with urinary leakage from the perineum [5]. A cystourethrogram shows the fistula tract.…”