A Longitudinal Study of Cognitive Abilities in Williams Syndrome

Porter, Melanie; Dodd, Helen F.

doi:10.1080/87565641.2010.549872

Cited by 17 publications

(48 citation statements)

References 18 publications

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“…Profiles and Development of Adaptive Behavior in Adolescents and Adults with Williams Syndrome strengths and weaknesses in WS were consistent, at least on those abilities assessed using the WJ-R COG [24].…”

Section: Trista Juhsin Fumentioning

confidence: 67%

Profiles and Development of Adaptive Behavior in Adolescents and Adults with Williams Syndrome

Fu¹

2015

IJIET

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Section: Trista Juhsin Fumentioning

confidence: 67%

Profiles and Development of Adaptive Behavior in Adolescents and Adults with Williams Syndrome

Fu¹

2015

IJIET

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“…In contrast to the preceding studies which included only child participants, the participants in the remaining study spanned a very broad age range. Porter and Dodd [] used the Woodcock–Johnson Tests of Cognitive Ability‐Revised [WJ‐R; Woodcock and Johnson, ] to assess the overall IQ and Cognitive Factor SSs of 27 individuals with WS at two time points about five years apart. The participants' CA at Time 1 ranged from 5.00–44.67 years with a mean of 16.16 years.…”

Section: Introductionmentioning

confidence: 99%

Children with Williams syndrome: Developmental trajectories for intellectual abilities, vocabulary abilities, and adaptive behavior

Mervis¹,

Pitts²

2015

American J of Med Genetics Pt C

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To examine longitudinal trajectories of intellectual abilities, single-word vocabulary abilities, and adaptive behavior for 76 children with Williams syndrome (WS) aged 4 – 15 years, we compared their standard scores (SSs) at two time points approximately 3 years apart on the same standardized measures. At the group level, mean SS declined significantly for 8 of the 12 measures and showed a slight (nonsignificant) increase or decrease for 4 measures. However, for most measures significant changes in SS were found for only a small proportion of the children, with some children evidencing significant declines and a smaller proportion evidencing significant increases. Significant SS changes were most common for adaptive behavior. For all measures, the mean magnitude of SS change was smaller for older children (> 7.5 years at Time 1) than for younger children (< 7.5 years at Time 1). Furthermore, correlations between Time 1 and Time 2 SSs were larger for the older cohort than for the younger cohort, indicating that SS stability was greater for older children than for younger children. Although mean SSs declined for most measures, indicating that children with WS as a group were not making the expected amount of progress relative to their general population peers who earned the same SS at Time 1, there was little evidence either of regression (loss of skills) or stagnation (failure to increase raw scores). The relations of these results to those of previous smaller-sample longitudinal studies of children with WS and the implications of the findings are considered.

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“…Though cognitive abilities range from moderate intellectual disability to average, WS is usually associated with mild to moderate cognitive impairment with typical IQ in the 50s–60s (e.g., Bellugi et al, 2000; see Martens et al, 2008 for a review). IQ appears to be relatively stable with age (Howlin et al, 1998; Porter and Dodd, 2011; Mervis et al, 2012) with greater verbal than spatial abilities (Bellugi et al, 1994). Receptive language abilities appear to be a relative strength in WS while other aspects of language are consistent with their cognitive profile (Brock, 2007).…”

Section: Introductionmentioning

confidence: 99%

(A)musicality in Williams syndrome: examining relationships among auditory perception, musical skill, and emotional responsiveness to music

Lense¹,

Shivers²,

Dykens³

2013

Front. Psychol.

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Williams syndrome (WS), a genetic, neurodevelopmental disorder, is of keen interest to music cognition researchers because of its characteristic auditory sensitivities and emotional responsiveness to music. However, actual musical perception and production abilities are more variable. We examined musicality in WS through the lens of amusia and explored how their musical perception abilities related to their auditory sensitivities, musical production skills, and emotional responsiveness to music. In our sample of 73 adolescents and adults with WS, 11% met criteria for amusia, which is higher than the 4% prevalence rate reported in the typically developing (TD) population. Amusia was not related to auditory sensitivities but was related to musical training. Performance on the amusia measure strongly predicted musical skill but not emotional responsiveness to music, which was better predicted by general auditory sensitivities. This study represents the first time amusia has been examined in a population with a known neurodevelopmental genetic disorder with a range of cognitive abilities. Results have implications for the relationships across different levels of auditory processing, musical skill development, and emotional responsiveness to music, as well as the understanding of gene-brain-behavior relationships in individuals with WS and TD individuals with and without amusia.

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A Longitudinal Study of Cognitive Abilities in Williams Syndrome

Cited by 17 publications

References 18 publications

Profiles and Development of Adaptive Behavior in Adolescents and Adults with Williams Syndrome

Profiles and Development of Adaptive Behavior in Adolescents and Adults with Williams Syndrome

Children with Williams syndrome: Developmental trajectories for intellectual abilities, vocabulary abilities, and adaptive behavior

(A)musicality in Williams syndrome: examining relationships among auditory perception, musical skill, and emotional responsiveness to music

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