A giant right atrial appendage aneurysm in an infant: A case report

Yue, Jianming; Wang, Qi; Liu, Bin; Zhou, Leng

doi:10.1111/echo.15350

Cited by 5 publications

(5 citation statements)

References 9 publications

(26 reference statements)

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“…10 This malformation is associated with significant morbidity; diagnostic imaging such as echocardiography and magnetic resonance imaging play a fundamental role in diagnosis, management, and follow-up. 16 The treatment is controversial and there is still no established consensus, however surgical resection is preferred in patients with symptoms or progressive enlargement in order to prevent complications such as thromboembolism, atrial arrhythmia, heart failure, and sudden death due to rupture. Conservative management with anticoagulants reduces the risk of thromboembolic events and is recommended in patients for whom surgery is contraindicated.…”

Section: Discussionmentioning

confidence: 99%

“…Conservative management with anticoagulants reduces the risk of thromboembolic events and is recommended in patients for whom surgery is contraindicated. 16 The AAA should form part of the differential diagnoses in cases where the abnormal chamber is adjacent to the atrium. 7 In addition, another differential diagnosis should be made in the case of fetal hydrops.…”

Section: Discussionmentioning

confidence: 99%

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Prenatal Diagnosis of a Right Atrial Appendage Aneurysm: Case Report and Review of the Literature

Miranda,

Villalobo,

Alfieri

et al. 2024

AJP Rep

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Introduction Congenital malformations of the right atrium are rare heart defects with only a few cases described prenatally. Early diagnosis of these anomalies is becoming increasingly important for proper follow-up and due to the possibility of serious complications such as supraventricular arrhythmia, thromboembolic events, and sudden death. Objective The atrial appendage aneurysm (AAA) is a dilatation of the atrial appendage. It is considered an extremely rare congenital anomaly. However, this condition is clinically significant because it leads to atrial arrhythmias, recurrent emboli, heart failure, and chest pain. In addition, it is possible to recognize AAA prenatally with fetal echocardiography, even if it rarely happens. However, few fetal AAA cases have been reported in the literature. Study Design We report a case of a fetal AAA; diagnosed prenatally and with postnatal confirmation. We undertook a systematic review of studies on fetal AAA to synthesize available knowledge on diagnosing and managing this rare condition. Results A total of eight studies describing 24 patients were identified and analyzed. Conclusion Despite their rarity, fetal atrial appendage aneurysms necessitate early detect on due to associated severe complications. Our findings emphasize the importance of prenatal diagnosis through fetal echocardiography and highlight the need for further research to optimize management strategies and improve outcomes for affected individuals.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Prenatal Diagnosis of a Right Atrial Appendage Aneurysm: Case Report and Review of the Literature

Miranda,

Villalobo,

Alfieri

et al. 2024

AJP Rep

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“…Some atrial tachyarrhythmias may persist after birth [ 12 ]. In one case report, the role of transesophageal echocardiography was considered to be very important because of the quality of information provided to the surgical team that operated on that patient [ 13 ].…”

Section: Discussionmentioning

confidence: 99%

A Gigantic Congenital Right Atrial Appendage Aneurysm in an Infant: Ten-Year Follow-Up

et al. 2022

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“…4,5 The first description of a right atrial appendage aneurysm (RAAA) occurred in 1947 and there have only been about 30 published cases. 6,7 The natural history, management, and long-term outcomes of LAAA and RAAA are not well understood given the paucity of published reports. 8 It is hypothesized that these patients are at a higher risk of atrial arrhythmias and thromboembolic complications due to the hemodynamic changes associated with an increased appendage orifice.…”

Section: Introductionmentioning

confidence: 99%

Atrial Appendage Aneurysms: Natural History and Outcomes

Penfold

Haq

Connolly

et al. 2023

World J Pediatr Congenit Heart Surg

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Background Left (LAAA) and right atrial appendage aneurysms (RAAA) are rare entities, and their natural history, management, and long-term outcomes are not well studied. Methods This retrospective review includes all patients from 2000 to 2021 with atrial appendage aneurysms at our institution identified using an electronic search tool. LAAA and RAAA were confirmed using multimodality imaging and intraoperative findings. Results We identified 13 (87%) patients with LAAA and 2 (13%) with RAAA. At diagnosis, 11 (73%) were female, mean age was 51.4 ± 18.8 years, and ejection fraction 56.5 ± 13.1%. Three (20%) patients had congenital heart disease including 2 (13%) with atrioventricular septal defects and 1 (7%) with congenitally corrected transposition. LAAA/RAAA was diagnosed due to new-onset atrial fibrillation (AF) in 6 (40%) patients and embolic stroke in 2 (13%). Ten patients had preexisting AF diagnosed 2.9 ± 1.4 years earlier at a mean age of 50.2 ± 15.5 years. Thrombus within the aneurysm was identified in 2 (15%) LAAA patients. All patients were on anticoagulation and follow-up of the cohort from diagnosis was 7.1 ± 6.2 years. Eleven (73%) patients were surgically managed with 7 (64%) lesions excised, 1 (9%) stapled, and 3 (27%) ligated. Postoperative complications occurred in 2 (18%) patients with 1 (7%) developing tricuspid regurgitation and another with pericardial effusion and tamponade. Conclusions Atrial appendage aneurysm is a rare disease and nearly half of patients present with AF. Surgical treatment with concomitant AF ablation is a reasonable and safe management option.

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A giant right atrial appendage aneurysm in an infant: A case report

Cited by 5 publications

References 9 publications

Prenatal Diagnosis of a Right Atrial Appendage Aneurysm: Case Report and Review of the Literature

Prenatal Diagnosis of a Right Atrial Appendage Aneurysm: Case Report and Review of the Literature

A Gigantic Congenital Right Atrial Appendage Aneurysm in an Infant: Ten-Year Follow-Up

Atrial Appendage Aneurysms: Natural History and Outcomes

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