A giant aneurysm of noncoronary sinus of Valsalva concomitant with aortic regurgitation and mitral regurgitation

Abstract

Aneurysms of the sinus of Valsalva (ASV) are rare, with an incidence ranging from 0.1% to 3.5% of all congenital cardiac defects and a prevalence of 0.009% in an autopsy series.ASVs occur much more frequently in the right coronary sinus of Valsalva. Previous reports, based on necropsy and cardiac surgery findings, estimated that 20% of ASVs are unruptured. Patients with an unruptured ASV may remain asymptomatic for a long period of time until rupture. They may also presented with dyspnea, palpitation, and angina-like chest pain. Aortic insufficiency in the patients with unruptured ASVs is common, and other valvular lesions can be observed in these patients as well. Echocardiography, as a noninvasive and portable tool, is widely used to detect ASVs. Additionally, computed tomography and cardiac magnetic resonance imaging, alone or in combination, can provide precise information about its anatomic extension and intrinsic characteristics of the pathology.

A Fatal Case of an Undiagnosed Ruptured Aneurysm of the Noncoronary Sinus of Valsalva

“…In this case, postmortem genetic testing was not performed. Other anomalies associated with ruptured SVA, such as atrial and ventricular septal defect, 4,5 bicuspid aortic valve, 4,5 pulmonary stenosis, 4 coarctation of the aorta, 5 and severe aortic insufficiency, 6 were not detected. The patient had no documented infective endocarditis before presentation.…”

Ruptured Coronary Sinus of Valsalva in the Setting of a Supracristal Ventricular Septal Defect

“…It represents 0.1-3.5% of all congenital heart diseases. 7 ASVs occur much more frequently in the right coronary sinus of Valsalva. Previous reports, based on necropsy and cardiac surgery findings, estimated that 20% of ASVs are unruptured.…”

Surgical Reconstruction of Valsalva Sinus Aneurysms: One Surgical Team Outcomes from Tertiary Center

“…Given the central position of aorta in the base of the heart, make it possible that SOVA could rupture any heart chamber, but mostly to the right ventricle or right atrium (2,8). Aortic Valve incompetence is common in patients with SVA, which occurs in 30 -50% of patients and it can influence on disease progression (9). For achieving good long-term results in patients with SVA it is important to correct concomitant AI which usually arises from the effect of concomitant VSD or from other aortic valve abnormality, including a bicuspid valve (10).…”