A Dislocated Crystalline Lens in a Patient With Marfan Syndrome

Abstract

A 46-year-old woman with Marfan syndrome presented with left crystalline lens dislocation due to zonular insufficiency. Her natural lenses had been noted to be partially subluxated when she was an infant, with spontaneous complete dislocation of her left lens over time. Her presenting visual acuity was 20/30 OU with aphakic spectacles. Her intraocular pressure levels were 26 mm Hg OD and 30 mm Hg OS. She underwent pars plana vitrectomy, lensectomy, and insertion of a scleral-fixated intraocular lens in the left eye. And intraoperative photograph (Figure ) shows the patient's dislocated native intraocular lens resting on the retina.Subluxation of the crystalline lens (ectopia lentis) is a common occurrence in patients with Marfan syndrome, with 60% of patients affected in 1 case series. 1 Complete, spontaneous posterior dislocation is a less common complication. [2][3][4]