A CLINICAL ANALYSIS OF MYOCLONUS EPILEPSY (UNVERRICHT‐LUNDBORG), MYOCLONIC CEREBELLAR DYSSYNERGY (HUNT) AND HEPATO. LENTICULAR DEGENERATION (WILSON)¹

Uraemic myoclonus: an example of reticular reflex myoclonus?

“…The myoclonus which occurred in both these patients with acute renal failure was clinically similar to the action or intention myoclonus described by Wolfhart and Hook (1951) and Lance and Adams (1963) in syndromes of different aetiology-that is, it was usually absent when the patient was at rest, but was provoked by any voluntary movement. Lance and Adams (1963) also demonstrated that a variety of sensory stimuli were capable of provoking a myoclonic response in their patients with postanoxic encephalopathy.…”

Myoclonus and ataxia occurring in a family

“…The mode of inheritance appears to be by an autosomal dominant gene of incomplete penetrance. DISCUSSION Since the original description by Ramsay Hunt in 1914, Wohlfart andHook (1951), Gilbert et al (1963), Aigner and Mulder (1960), Bradshaw (1954), Noad and Lance (1960), and Harriman and Millar( 1955) have described a variety of syndromes in-F cluding dyssynergia, myoclonus, and epilepsy. The existence of a variant of the Ramsay Hunt syndrome, i.e., progressive cerebellar dyssynergia, myoclonus, and without epilepsy, was recognized by Ramsay Hunt (1921), Wohlfart and Hook (1951), and Gilbert et al (1963), and is unlike the disorder described by Unverricht (1891) and Lundborg (1903) because of the absence of mental deterioration and epilepsy.…”

Psychiatric Aspects of Myoclonus Epilepsy

“…Case reports of patients with myoclonus epilepsy have been described by other authors : Clark and Prout (1902), Dana (1903), Grinker, Serota and Stein (1938), Medlicott (1943), Wohlfart and Hook (1951), Bradshaw (1954), Harriman, Millar and Stevenson (1955), Kreindler et al (1959) and Noad, Lance and Walsh (1960). Hodskins and Yakolev (1930) review all the pathological material until 1928.…”