A case of splenogonadal fusion accompanied by accessory spleen in a 4-year-old boy

Abstract

Splenogonadal fusion (SGF) is a rare benign malformation in which spleen is aberrantly attached to the gonads or mesonephric derivatives. This entity often presents with scrotal mass, inguinal hernia, or cryptorchidism. Herein, we report our experience with a boy who presented with a scrotal enlargement which later turned out to be SGF. Moreover, an accessory spleen was unexpectedly found in the left inguinal canal. To the best of our knowledge, this is the first report of SGF and accessory spleen in the literature. Although rare, SGF should be included in the complete differential diagnosis list of scrotal masses, especially in children. The use of frozen section pathology if available would aid the surgeon in avoiding unnecessary orchiectomy in small testicular masses of benign origin.

Splenogonadal fusion: a case report of three cases and a literature review

“…In a case of SGF presenting as a testicular tumor, it was reported that dynamic observation was continued only after a biopsy of the mass. Subsequently, the diagnosis of discontinuous splenogonadal fusion was made ( 18 ). A fibrous capsule can be clearly observed between the testes and the spleen in both the continuous and the discontinuous types.…”

Accessory spleen misdiagnosed as left adrenal tumor causing complications

“…The accessory spleen is caused by the fusion failure of the splenic anlage located in the dorsal mesogastrium in the fth week of fetal life [4] or developed from the deciduous part of the main spleen [5].…”