A case of pararenal PEComa with extensive bone metaplasia

Menendez, Carmen L.; Ugarteburu, Rodrigo Gil; Ampudia, Jesús María Capilla; Torres, Gabriela Corte; Fuente, Eduardo; Argüelles, Mario

doi:10.1007/s00428-008-0581-1

Cited by 1 publication

(2 citation statements)

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“…Abdominal and pelvic CT (3 months) abdominal ultrasound (6 months and 1 year) and abdominal CT (4th year) showed no signs of local or distant disease. Besides the common benign evolution some PEComas had unfavourable course with metastatic disseminations (lung, liver, bone and abdominal wall)2 4 6; however, in vast majority of published data sclerosing PEComas have benign course, which is in agreement with the presented case.…”

Section: Outcome and Follow-upsupporting

confidence: 91%

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Pararenal sclerosing PEComa

et al. 2013

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Small renal or pararenal masses and retroperitoneum lesions are extremely difficult to diagnose. Imaging technology is a precious diagnostic tool; however, it places physicians in a difficult position since many lesions are not precisely diagnosed. Clinical and radiological findings can guide suspicion towards the diagnosis; however, in our current practice most diagnoses are based on histological findings. We aim to present a pararenal sclerosing perivascular epithelioid cell tumour (PEComa), a rare entity, whose diagnosis is only possible through invasive approaches and histological analysis. This rare lesion not only is difficult to diagnose but also has an uncertain behaviour, which is of major importance concerning its follow-up and prognosis. This case report is an attempt to add more data that will help establish criteria for diagnosis and follow-up of this rare disease.

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Section: Outcome and Follow-upsupporting

confidence: 91%

“…There are few published cases of pararenal sclerosing PEComas 4 8 and known data confirm the difficulty for diagnosis and follow-up for this entity.…”

Section: Discussionmentioning

confidence: 96%