A schwannoma is a benign tumor derived from Schwann cells existing around the nerve. It is capable of occurring anywhere in the whole body in the area where medullated nerves are distributed. 1-3 Around 25%-40% of schwannomas occur in the head and neck region and, of these, 1%-12% affect the intraoral area. 1 The most common site of oral schwannoma is the tongue, followed by the palate and buccal mucosa. 4,5 However, few of the features of tongue schwannomas have been specified in the literature to date. We report a case of schwannoma of the tongue and, since there is no recent review of tongue lesions in the Japanese literature we review the research available on this type of schwannomas clinicopathologically. Our review and other reviews published so far in international journals will be considered together in the discussion. 2 | MATERIAL S AND ME THODS We reviewed case reports and original articles on tongue schwannoma published up to March 2019. All identified cases were diagnosed and treated in Japan. The paper search was conducted in PubMed and Ichushi using "tongue" AND "schwannoma" (search 1) and "tongue" AND "neurilemmoma" (search 2) as keywords. Reports containing only abstracts were excluded. The examination items included gender, age, chief complaint, disease duration, subsite, depth (vertical position), size (maximum diameter), clinical findings, treatment, histopathological findings, and prognosis. Magnetic resonance imaging (MRI) findings were considered when MRI was performed. Chief complaints were divided into four categories: awareness of the mass; discomfort; tongue-specific dysfunction, such as movement disorder, dysphagia, dysarthria, or dyspnea; and pain. Subsites were designated as the movable tongue (MT) and base of the tongue (BT); the former was then subclassified as either lateral, dorsal, apex, or sublingual.