A Case of Felty's Syndrome With Portal Hypertension

A case of idiopathic portal hypertension associated with rheumatoid arthritis

“…The six cases of IPH associated with RA, including the present case, are shown in Table 1. In one of them IPH was associated with Felty's syndrome, 26 and in another with SLE and pulmonary hypertension. 8 In these cases the period between onset of RA and diagnosis of IPH ranged from 8 to 24 years.…”

“…During the last 20 years in Japan, 11 cases of IPH have been reported to be associated with systemic lupus erythematosus (SLE), 3,4,7-15 7 with mixed connective tissue disease, 2,5,16-20 2 with Sjögren syndrome, 21,22 4 with systemic sclerosis, 23-25 and 5 with RA. 8,[26][27][28][29] The cases of IPH associated with RA have been reported only from Japan. We suppose that the concept of IPH was created in Japan, considering that the same disease is termed noncirrhotic portal fibrosis in India 30 and hepatoportal sclerosis in the United States.…”