A case of febrile ulceronecrotic Mucha‐Habermann disease responsive to systemic corticosteroids

Abstract

Febrile ulceronecrotic Mucha‐Habermann disease (FUMHD) is a rare, potentially fatal subtype of pityriasis lichenoides et varioliformis acuta (PLEVA). Herein, we present a rare case of a 14‐year‐old male without significant past medical history who was diagnosed with FUMHD without a clear inciting factor. He was effectively treated with systemic corticosteroids with complete resolution of symptoms.

Febrile ulceronecrotic Mucha-Habermann disease - a case and treatment review

“…To our knowledge, only 135 cases of FUMHD have been previously described in literature, 43 in children and 92 in adults [6][7][8][9]. This rare disease is more prevalent in males (75%) and mostly affects children and young adults, having an estimated overall mortality rate of 12%.…”