Surgical strategies and outcomes of congenital supravalvular aortic stenosis

Liu, Hongli; Gao, Beibei; Sun, Qiang; Du, Xin; Pan, Yanjun; Zhu, Zhongqun; He, Xiaomin; Zheng, Jie

doi:10.1111/jocs.13213

Cited by 17 publications

(18 citation statements)

References 35 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…On the other hand, Liu et al (16) identified male gender, preoperative aortic stenosis, and peak gradient of ≥ 90 mmHg as risk factors for residual aortic stenosis while age < 2 years, bicuspid aortic valve, and diffuse type aortic stenosis were not.…”

Section: Discussionmentioning

confidence: 99%

“…However the short duration of follow-up, such as in this study (average of 8 years) may be misguiding when considered that reoperations are needed typically after a decade. However, prior studies have determined pulmonary arterial stenosis as a risk factor for mortality in the long term and catheter interventions, and highlighted the importance of close follow-up (13)(14)(15)(16) . Although some authors observed a decrease of more than 10mmHg or normalization of the gradient over the stenotic site in the majority of patients, generally balloon angioplasty is commonly utilized in order to achieve an intended relief (15,16) .…”

Section: Discussionmentioning

confidence: 99%

“…On the other hand, aortic regurgitation may occur after surgical treatment even in a valve with usual function and morphology. Although the degree of aortic regurgitation improves after surgical correction, aortic valve replacement, for this reason, is not uncommon and has been reported by numerous authors so far (2)(3)(4)(5)(6)(7)(8)(9)(12)(13)(14)(15)(16)(17) .…”

Section: Discussionmentioning

confidence: 99%

See 2 more Smart Citations

Evaluation of Supravalvular Aortic Gradient Changes Following Inverted Y-Patch Repair

Akkaya¹,

Bilen²,

Tuncer³

et al. 2020

BUCH

View full text Add to dashboard Cite

Objective: This study presents our single-institute experience regarding the patients who underwent surgical correction via inverted Y-patch repair with the diagnosis of supravalvular aortic stenosis. Method: A total of 16 patients who underwent inverted Y-patch (Doty) repair in our center between 2005 and 2019 were retrospectively analyzed. Complications, supravalvular residual gradient measurements, causes of re-operation were evaluated. Results: Patient population consisted of 9 males, 7 females with an overall mean age of 41.18±16.14 months (range: 4 months to 19 years). Eight (50%) patients were diagnosed with Williams-Beuren syndrome and 3 (18.7%) with bicuspid aortic valve. Three (18.7%) patients had undergone simultaneous subaortic membrane resection and pulmonary patch plasty was performed in 2 (12.5%) patients. There was one (6.7%) inhospital death and no mortality was observed during follow-up. The mean follow-up time was 5.25±3.37 years. During this period, 2 (12.5%) patients required pulmonary balloon dilatation and one patient repeated Doty repair and aortic valve commissurotomy two years after the initial surgery. Thereafter the same patient needed aortic homograft valve replacement and Doty repair for the third time due to severe aortic insufficiency and suprvalvular aortic stenosis. Conclusion: Inverted Y-patch repair provides satisfactory results, acceptable reoperation risk, and good overall survival.

show abstract

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

Evaluation of Supravalvular Aortic Gradient Changes Following Inverted Y-Patch Repair

Akkaya¹,

Bilen²,

Tuncer³

et al. 2020

BUCH

View full text Add to dashboard Cite

show abstract

“…young adults but may also occur as a complication of a type A aortic dissection due to a large thrombosed false lumen which compresses the true lumen. [1][2][3] We present the images of a patient who developed heart failure following a SAS due to a chronic type A aortic dissection. Two months following surgery, his BNP decreased to 755 pg/mL, and an echo showed that his LVDd decreased to 63 mm and his ejection fraction improved to 42%.…”

Section: Supravalvular Aortic Stenosis (Sas) Is Usually Seen In Childmentioning

confidence: 99%

“…Supravalvular aortic stenosis (SAS) is usually seen in children and young adults but may also occur as a complication of a type A aortic dissection due to a large thrombosed false lumen which compresses the true lumen . We present the images of a patient who developed heart failure following a SAS due to a chronic type A aortic dissection.…”

mentioning

confidence: 99%

Supravalvular aortic stenosis with a chronic type A aortic dissection

2018

View full text Add to dashboard Cite

Influence of Surgical Methods on Hemodynamics in Supravalvular Aortic Stenosis: A Computational Hemodynamic Analysis

Liu

Jiang

et al. 2021

Pediatr Cardiol

View full text Add to dashboard Cite

We compared differences in the hemodynamic parameters of multiple surgical techniques for supravalvular aortic stenosis (SVAS). A three-dimensional model was reconstructed based on a patient's CT scan. Virtual McGoon, Doty, and Brom repairs were completed using computer-aided design (CAD). Hemodynamic parameters were calculated through computational fluid dynamics (CFD). The velocity profile and wall shear stress (WSS) showed the blood flow pattern. Energy loss (EL) and energy efficiency (EE) were calculated to estimate the cardiac workload. The perioperative blood flow ratio (BFR) of brachiocephalic vessels and coronary arteries was calculated. The preoperative flow velocity was abnormally high (> 5.0 m/s). High WSS was detected at the sinotubular junction (STJ), and its preoperative distribution in the aorta was uneven. High-speed flow disappeared after each of the three operations. The WSS distribution at the aortic root was consistent with the postoperative STJ structure of each operation. EL in the systolic phase decreased postoperatively (Original: 634 mW, McGoon: 218 mW, Doty: 278 mW, Brom: 255 mW). No significant difference in brachiocephalic BFR was detected among the different techniques. A slightly increased coronary BFR (Original: 7.56%, McGoon: 7.99%, Doty: 8.55%, Brom: 8.89%) was detected. McGoon, Doty, and Brom repair each effectively restored stable blood flow and greatly improved EE. The best WSS distribution and coronary blood supply were achieved after Brom repair due to its ability to reconstruct the symmetrical aortic root structure. CFD combined with a virtual operation is a promising method in surgical planning and optimization for SVAS.

show abstract

Surgical strategies and outcomes of congenital supravalvular aortic stenosis

Cited by 17 publications

References 35 publications

Evaluation of Supravalvular Aortic Gradient Changes Following Inverted Y-Patch Repair

Evaluation of Supravalvular Aortic Gradient Changes Following Inverted Y-Patch Repair

Supravalvular aortic stenosis with a chronic type A aortic dissection

Influence of Surgical Methods on Hemodynamics in Supravalvular Aortic Stenosis: A Computational Hemodynamic Analysis

Contact Info

Product

Resources

About