Beta-thalassemia in the paediatric cardiac surgery setting - a case report and literature review

Abstract

Beta (β)-thalassemia is a blood disorder with an incidence of 1 in 100,000. This case report outlines a patient with β-thalassemia requiring cardiopulmonary bypass (CPB) and the measures taken to ensure an uneventful procedure.

تقييم بعض انزيمات القلب والحديد في مصل مرضى بيتا-ثلاسيميا في مدينة ذي قار ، العراق

“…It ultimately results in a lack of developed erythrocytes. Additionally, it has been demonstrated that compared to normal erythrocytes, β-thalassemic erythrocytes have a haemolysis percentage that is approximately 115% higher 2 . This is the cause of the anemia and hypoxia symptoms that thalassemic individuals experience 3 .…”

Voices of Spring

“…1 In children, are there new methods mandating a re-evaluation for blood conservation, allowing bloodless surgery in children, 2 should modified ultrafiltration be used in congenital heart disease 3 or how do we best care for those with a blood disorder that reduces the production of hemoglobin, such as beta-thalassemia? 4 How is temperature managed in different parts of the world? 5 Unique case studies can be the gateway for additional study: epoprostenol for treating oxygenator pressure drop, 6 bivalirudin use in a patient with heparin-induced thrombocytopenia in renal failure.…”