A 52-year-old woman with tetralogy of Fallot status post-complete surgical repair with infundibular resection, pulmonary valvotomy, and patch closure of the ventricular septal defect presented with severe pulmonary regurgitation and depressed right ventricular function. During intended percutaneous pulmonary valve implantation (PPVI), multiple stenotic lesions were discovered in her left anterior descending (LAD) coronary artery, and the procedure was aborted. She underwent treatment of these lesions using drug-eluting stents by our adult interventional colleagues and returned to the congenital catheterization laboratory for PPVI 18 months following her initial procedure. Given the potential risk of crush injury to the coronary arterial stents, the distal LAD artery was continuously monitored during the procedure via a pressure wire with the capability of re-expanding the stent if needed.Copyright © 2017 Science International Corp.
Key Words
Congenital catheterization • Intervention • Valve implantation
IntroductionPercutaneous pulmonary valve implantation (PPVI) is an effective method for treating right ventricular outflow tract (RVOT) obstruction and regurgitation in patients with congenital heart disease [1,2,3]. A rare but catastrophic complication of PPVI is mechanical coronary artery compression due to implantation of a stent and/or valve within the RVOT [4]. Coronary artery testing is recommended during balloon angioplasty of the RVOT to assess coronary artery compression or distortion. However, the presence of an existing coronary artery stent may render coronary artery testing with balloon angioplasty/compliance testing a higher risk procedure. Here, we report the first use of a pressure wire within a stented left anterior descending (LAD) coronary artery in close proximity to the RVOT during PPVI to assess for coronary artery stent compromise and to maintain access for treatment of compression with redilation of the stent or re-stent if necessary.
Case PresentationA 52-year-old woman with tetralogy of Fallot presented to our adult congenital cardiology program for evaluation. She underwent complete surgical repair at 8 years of age consisting of infundibular resection, pulmonary valvotomy, and patch closure of a ventricular septal defect. Her residual atrial septal defect was closed with a CardioSEAL™ Occlusion Device (Nitinol Medical Technologies, Ind., Boston, Massachusetts) at 38 years of age. Past medical history was also significant for diabetes mellitus and hypertension. As a result of her surgical palliation, the patient had severe pulmonary valve regurgitation with decreased right ventricular function and was referred for PPVI. Prior to RVOT intervention, multiple stenotic lesions were discovered within her LAD, and the procedure was aborted (Figure 1). Over the next few months, the patient underwent percutaneous coronary intervention by our adult interventional colleagues with a total of three drug-eluting stents placed along her proximal, mid, and distal LAD. After surveillance corona...