Nasal septal lipoma in a child: Pai syndrome or not?

AbdollahiFakhim, Shahin; Bayazian, Gholamreza; Notash, Rezvan

doi:10.1016/j.ijporl.2014.01.027

Cited by 7 publications

(10 citation statements)

References 18 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…In our case, the intracranial lipoma grew a little until the patient was 7 years. In previous studies, no neurological problems were reported in teenage cases (Coban et al, 2003;Szeto et al, 2005;Lederer et al, 2012;AbdollahiFakhim et al, 2014). However, they did not assess cognitive disabilities.…”

Section: Discussionmentioning

confidence: 92%

“…In our case, we obtained consistent cosmetic results after repair in infancy; however, the residual adipose mass in the septum grew gradually and obstructed the left nasal airway, which needed surgery. AbdollahiFakhim et al (2014) reported that a 12-year-old patient complained of nasal obstruction with residual nasal polyp, despite polyp resection at 2 months of age. We suggest that careful and long-term follow-up is needed for a septal polyp because the residual adipose mass in the septum can grow and obstruct the airway.…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

Mental Development and Surgical Prognosis of Pai Syndrome: A Case Report and Review of the Literature

Imai

Kure

Nara

et al. 2018

The Cleft Palate-Craniofacial Journal

View full text Add to dashboard Cite

Pai syndrome is a rare congenital disorder, and there are few reports about the long-term prognosis of mental development and surgical results. Here, we report a patient with Pai syndrome who was followed up from birth up to the age of 8 years. Additionally, we review 32 articles and discuss the long-term prognosis of Pai syndrome. In our case, an intracranial lipoma grew a little, but neither epilepsy nor intellectual disabilities occurred. However, she showed attention-deficit/hyperactivity disorder. Furthermore, her nasal airway was gradually obstructed by a residual intranasal polyp.

show abstract

Section: Discussionmentioning

confidence: 92%

Section: Discussionmentioning

confidence: 99%

Mental Development and Surgical Prognosis of Pai Syndrome: A Case Report and Review of the Literature

Imai

Kure

Nara

et al. 2018

The Cleft Palate-Craniofacial Journal

View full text Add to dashboard Cite

show abstract

“…3,4 Lipoma of the nasal cavity is rare and is mostly reported in children as a single mass or a piece of a syndrome. [5][6][7] There are few reports of lipomas in different parts of the nose, including nasopharynx, vestibule, nasal dorsum, and inferior turbinate. 4,[8][9][10][11][12] Patients may be asymptomatic, or like other masses occurring in sinuses and nasal cavity, they may present with symptoms, including nasal obstruction, facial edema, tenderness, rupture, and hemorrhage.…”

Section: Discussionmentioning

confidence: 99%

“…Thirteen percent of lipomas occur in head and neck, which the posterior neck, chicks, tongue, floor of the mouth, and buccal sulcus are the most common 3,4 . Lipoma of the nasal cavity is rare and is mostly reported in children as a single mass or a piece of a syndrome 5‐7 . There are few reports of lipomas in different parts of the nose, including nasopharynx, vestibule, nasal dorsum, and inferior turbinate 4,8‐12 .…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

Lipoma of the nasal septum: A case report

Jahandideh

Firouzabadi

et al. 2020

Clinical Case Reports

View full text Add to dashboard Cite

show abstract

Diagnostic criteria in Pai syndrome: results of a case series and a literature review

Morice

Galliani

Amiel

et al. 2019

International Journal of Oral and Maxillofacial Surgery

View full text Add to dashboard Cite

Pai syndrome was originally described as the association of a midline cleft lip, midline facial polyps, and lipoma of the central nervous system. However, only a few patients present with the full triad, and most exhibit a wide spectrum of phenotypic variability. The aim of this study was to phenotypically delineate Pai syndrome and to propose new criteria to facilitate a clinical diagnosis in the future. The study cohort consisted of seven case patients and an additional 60 cases diagnosed with Pai syndrome identified in a literature review. Only 23 of 67 patients presented the full triad as historically described by Pai et al. (1987). A congenital facial midline skin mass was always encountered, particularly affecting the nasal structures (60/67). A midline facial cleft was reported in 45 of 67 patients and a pericallosal lipoma in 42 of 67 patients. The proposed definition of Pai syndrome is the association of (1) a congenital nasal and/or mediofrontal skin mass and/or a mid-anterior alveolar process polyp as a mandatory criterion, and at least one of the following criteria: (2) midline cleft lip and/or midline alveolar cleft, and/or (3) a pericallosal lipoma or interhemispheric lipoma in the case of corpus callosum dysgenesis.

show abstract

Nasal septal lipoma in a child: Pai syndrome or not?

Cited by 7 publications

References 18 publications

Mental Development and Surgical Prognosis of Pai Syndrome: A Case Report and Review of the Literature

Mental Development and Surgical Prognosis of Pai Syndrome: A Case Report and Review of the Literature

Lipoma of the nasal septum: A case report

Diagnostic criteria in Pai syndrome: results of a case series and a literature review

Contact Info

Product

Resources

About