Untitled

Abstract

Authors review the case history and follow-up of a rare malignant fibrous histiocytoma patient, based on the relevant literary data. The tumour filled the retroperitoneum on the right side, in front of the right kidney. Intravenous urography and computer tomography revealed a 10 x 15 cm sized mass, suspect of being a kidney tumour. Upon surgery, the tumour was found to be a retroperitoneal malignant fibrous histiocytoma. In connection with the case, a brief review is given of the storiform type of malignant fibrous histiocytoma, regarding its aetiological, clinical and pathological aspects, the difficulties in diagnosis, as well as the therapeutic possibilities. Authors regard their case worthy of publication because of the retroperitoneal location and significant size of the tumour, and because of the unproven diagnosis prior to surgery. Even after 4 years the patient is symptom- and complaint-free, and CT has revealed no metastases.

Retroperitoneal Malignant Fibrous Histiocytoma Can Mimic a Hydatid Cyst

“…The tumor tissue may also comprise tumor giant cells, inflammatory cells, and xanthoma cells. The tumor may be interspersed with myxoid substance and elastic fibers [5]. …”

“…The histological differential diagnosis of MFH includes leiomyosarcoma, liposarcoma, and rhabdomyosarcoma. MFH is most frequent in those older than 70 years, and it rarely occurs under the age of 40 [5]. …”

“…Bertoni et al observed recurrence in 37.5% of cases. The 5-year survival rate was 36% according to Pezzi et al while Enziger et al observed recurrence in 25% and metastasis in 34%, with a recovery rate of 50% [5]. …”