Massive hemorrhage due to spontaneous rupture of a renal angiomyolipoma is a rare, but the most severe complication of this unusual tumor.
The aim of this publication is to present a rare case of massive retroperitoneal hemorrhage and hemoperitoneum due to spontaneous rupture of giant renal angiomyolipoma.
Case presentation: A 20-year-old woman, with a previous diagnosis of tuberous sclerosis and sudden onset of severe abdominal pain is presented. Median laparotomy on emergency was performed, with operative finding of hemoperitoneum and a giant ruptured retroperitoneal tumor with retroperitoneal hematoma. Gross pathology and histological examination determined the origin of the retroperitoneal tumor mass – angiomyolipoma, complicated with rupture and severe bleeding.
In conclusion, this case presents rare, but the most severe complication of renal angiomyolipomas – spontaneous rupture of the tumor with life-threatening retroperitoneal bleeding.