Diferenças entre Duas Condições Cardíacas Hipertróficas Distintas: Doença de Fabry Versus Cardiomiopatia Hipertrófica
Onur Akhan,
Mehmet Kış,
Tuncay Güzel
et al.
Abstract:Resumo
Fundamento
A cardiomiopatia hipertrófica (CMH) e a doença de Fabry (DF) são doenças herdadas geneticamente com características fenotípicas de hipertrofia ventricular esquerda (HVE) que causam resultados cardíacos adversos.
Objetivos
Investigar as diferenças demográficas, clínicas, bioquímicas, eletrocardiográficas (ECG) e ecocardiográficas (ECO) entre CMH e DF.
Métodos
60 pacientes com CMH e 40 pacientes com DF foram anali… Show more
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