Congenital nasal pyriform aperture stenosis with single central megaincisor

Fonseca, Eduardo Kaiser Ururahy Nunes; Murakoshi, Rodrigo Watanabe; Loureiro, Rafael Maffei; Sumi, Daniel Vaccaro; Soares, Carolina Ribeiro; Gomes, Regina Lúcia Elia; Daniel, Mauro Miguel; Funari, Marcelo Buarque de Gusmão

doi:10.31744/einstein_journal/2019ai4525

Cited by 1 publication

(3 citation statements)

References 6 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Chromosomal abnormalities with HPE genes have been reported in some cases [3]. Pyriform aperture stenosis occurs due to embryological malformations of the primary palate, which are associated with a hard triangular-likepalate and the bone over growth of the nasal process of the maxilla [4]. CNPA scan be isolated or often is associated with other malformations mainly the triangular-shape palate and the single central megaincisor, which is found in up to 75% of these patients [4] such as the case of our patient.…”

Section: Discussionmentioning

confidence: 99%

“…Close follow up until growing expansion of the nasal cavity is essentail. Surgical interventions are reserved for cases with severe stenosis after conservative treatment [4,8].…”

Section: Discussionmentioning

confidence: 99%

“…Dilatation is considered appropriate when a 3.5 mm endotracheal tube can be passed [4]. The evolution is progressively favorable in parallel with the growth of the bones of the nose and the spacing of the two processes which cause the narrowing.…”

Section: Discussionmentioning

confidence: 99%

See 2 more Smart Citations

A Rare Cause of Neonatal Respiratory Distress: Congenital Stenosis of Piriform Aperture

Bouatay¹

2019

OHNS

View full text Add to dashboard Cite

Congenital Nasal Pyriform Aperture Stenosis (CNPAS), is a very rare cause of neonatal upper airway obstruction [1]. Its prevalence remains unknown (a few isolated cases were described in literature). It can be isolated or sometimes associated to other midline defects. The diagnosis is suggested by physical examination and confirmed by Computer Tomography (CT) findings. Therapeutic approach depends on the severity of the stenosis [2]. We report a case of CNPAS to highlight the importance of recognizing the classic signs of CNPAS on cross-sectional imaging to prevent fatal out come and to present our experience in the non-surgical management of this rare anomaly. Observation We report the case of a full-term female new born, resulting from a pregnancy of normal course with vaginal delivery term at a private

show abstract

Section: Discussionmentioning

confidence: 99%

“…Close follow up until growing expansion of the nasal cavity is essentail. Surgical interventions are reserved for cases with severe stenosis after conservative treatment [4,8].…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

A Rare Cause of Neonatal Respiratory Distress: Congenital Stenosis of Piriform Aperture

Bouatay¹

2019

OHNS

View full text Add to dashboard Cite

show abstract

Congenital nasal pyriform aperture stenosis with single central megaincisor

Cited by 1 publication

References 6 publications

A Rare Cause of Neonatal Respiratory Distress: Congenital Stenosis of Piriform Aperture

A Rare Cause of Neonatal Respiratory Distress: Congenital Stenosis of Piriform Aperture

Contact Info

Product

Resources

About