Case for diagnosis

Abstract

Ketron-Goodman disease was formerly considered a disseminated type of pagetoid reticulosis. However, according to the new classification consensus, it should be regarded as aggressive epidermotropic CD8 T-cutaneous lymphoma, cutaneous gamma/delta T-lymphoma, or tumor-stage mycosis fungoides, depending on the clinical-histological picture. This case highlights a rare and challenging presentation of Ketron-Goodman disease with an indolent presentation and evolution and good response to a low-grade treatment regimen, not fitting well into the new classification criteria.

Pagetoid Reticulosis: Report of Two Cases and Review of the Literature

“…Recently documented cases of PR [ 12 , 13 , 14 , 15 , 16 , 17 ] have included patients of all ages, including children. Localized perioral lesions have also been reported [ 18 ] as well as a generalized form of the disorder known as Ketron-Goodman disease [ 19 ].…”