A Giant Mesenteric Fibromatosis Case Presenting with Mechanical Intestinal Obstruction and Successfully Resected with Partial Duodeno-Jejunectomy and Right Hemicolectomy

Polat, Coşkun; Aktepe, Fatma; Türel, Serkan; Özkeçeci, Taner; Arýkan, Yuksel

doi:10.1590/s1807-59322010000100017

Cited by 17 publications

(37 citation statements)

References 15 publications

(27 reference statements)

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“…The imaging studies in the work up of our case were inconclusive. Differential diagnoses include GIST, lymphoma, carcinoid tumour, fibrosarcoma or inflammatory fibroid polyp [1]. In our case, CECT abdomen revealed hypodense (+25HU) and mildly enhancing (+46HU) focal lesion in intraperitoneal cavity with retroperitoneal extension with a possibility of leiomyoma or GIST.…”

Section: Discussionmentioning

confidence: 57%

“…women, often during and after pregnancy [1,3]. Desmoid tumours (DT) are histologically benign, but they may show local recurrence after excision [3].…”

Section: Discussionmentioning

confidence: 99%

“…The term 'desmoid' was coined by Muller in 1838 and was derived from Greek word 'desmos' meaning band or tendon [1]. These are rare tumours, arising from musculo-aponeurotic elements accounting for about 0.03% of all neoplasm and 3.5% of all fibrous tissue neoplasm [2].…”

Section: Discussionmentioning

confidence: 99%

“…They are classified into three types: abdominal, extra abdominal and intra abdominal [1]. Intra abdominal desmoid or fibromatosis is rare, locally aggressive mesenchymal tumour that usually develops in the mesentery or retro-peritoneum [4].…”

Section: Discussionmentioning

confidence: 99%

“…End to end anastomosis was done and specimen was sent for histopathology which confirmed the diagnosis of MF. Considering the rarity of this tumour and difficulties in diagnostic and therapeutic ambit, we believe it is justified to describe this case which came to our observation.women, often during and after pregnancy [1,3]. Desmoid tumours (DT) are histologically benign, but they may show local recurrence after excision [3].…”

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confidence: 99%

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Mesenteric Fibromatosis (Desmoid Tumour) - A Rare Case Report

2014

JCDR

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A 29-year-old male presented with complaints of swelling in the right side of umbilicus for six months associated with dull ache for two months. It was gradually increasing in size and there was no other symptom. There was no significant past or family history.A globular intraperitoneal lump approx 5x4 cm was found in umbilical region which was firm, mobile, and mildly tender with smooth surface and margin, no fixity but not moving with respiration. Ultrasonography (USG) of whole abdomen showed it as intra abdominal abscess or cyst. Fine needle aspiration cytology revealed a few monolayered clusters of colonic mucosal cells, some muscle fibres and mucin strings in the background of blood with no atypical or malignant cells. Contrast enhanced computerized tomography Revealed an oval hypodense (+25 HU) and mildly enhancing (+46 HU) focal lesion in intraperitoneal cavity with retroperitoneal extension suggestive of leiomyoma or GastroIntestinal Stromal Tumour. Colonoscopy and endoscopy showed no polyps.Exploratory laparotomy revealed a mass 6x5x4 cm [Table/ Fig-1] in ileal mesentery. It was excised along with 20cm of ileum and end to end anastomosis in two layers.Histopathologically [Table/ Fig-2], a lesion in the subepithelium composed of cells with blunt ended nuclei arranged in sheets, fascicles, whorl and haphazard patterns was found. Hyalinised capillaries were interspersed with focal lymphocytic infiltration and cells with moderate nuclearr atypia in peripheral areas characterized MF. Postoperative days were uneventful and discharged on 10 th day. Adjuvant radiotherapy (50 Gy) was given to our patient in the post operative period. Follow up for three years which included USG abdomen and colonoscopy didn't reveal any new pathological lesions. DISCUSSIONThe term 'desmoid' was coined by Muller in 1838 and was derived from Greek word 'desmos' meaning band or tendon [1]. These are rare tumours, arising from musculo-aponeurotic elements accounting for about 0.03% of all neoplasm and 3.5% of all fibrous tissue neoplasm [2]. It is commonly seen in reproductive years of A 29-year-old male presented with a swelling on the right side of the umbilicus for six months and dull aching pain for two months. Fine needle aspiration cytology, ultrasonography, contrast enhanced computerized tomography findings were inconclusive. After Exploratory laparotomy, a mass approx 6x5x4 cm in ileal mesentery was identified and excised along with 20cm of ileum. End to end anastomosis was done and specimen was sent for histopathology which confirmed the diagnosis of MF. Considering the rarity of this tumour and difficulties in diagnostic and therapeutic ambit, we believe it is justified to describe this case which came to our observation.women, often during and after pregnancy [1,3]. Desmoid tumours (DT) are histologically benign, but they may show local recurrence after excision [3].

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Section: Discussionmentioning

confidence: 57%

“…women, often during and after pregnancy [1,3]. Desmoid tumours (DT) are histologically benign, but they may show local recurrence after excision [3].…”

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

mentioning

confidence: 99%

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