2009
DOI: 10.1590/s1806-37132009000200015
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Simultaneous bilateral spontaneous pneumothorax in an adult patient with cystic fibrosis

Abstract: Pneumothorax is a common complication in cystic fibrosis and is associated with worsening of lung function. However, bilateral simultaneous pneumothorax in cystic fibrosis is a rare condition. We describe the case of a 17-year-old female with cystic fibrosis who presented with spontaneous pneumothorax. Clinically, she presented right-sided chest pain and progressive breathlessness. The pneumothorax failed to resolve after the initial treatment (chest drainage). However, the patient was later successfully treat… Show more

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“…πλήζσο εκθαλίδεηαη ζε αζζελείο ειηθίαο κεγαιχηεξεο ησλ 18 ρξφλσλ κε FEV 1 κηθξφηεξε ηνπ 40% ηεο πξνβιεπφκελεο ηηκήο.Άιινη επηβαξπληηθνί παξάγνληεο είλαη ε παξνπζία P. aeruginosa, Burkholderia cepacia θαη εηδψλ Aspergillus89 . Ζ ζεξαπεία ηνπ πλεπκνζψξαθα ζηνρεχεη ηφζν ζηελ αζθαιή θαη απνηειεζκαηηθή ιχζε ηνπ, φζν θαη ζηελ πξφιεςε ππνηξνπήο ηνπ90 . Οη κηθξνί Οη παξαξξηλνθνιπίηηδεο απνηεινχλ ηηο ζπλεζέζηεξεο θιηληθέο εθδειψζεηο απφ ην αλψηεξν αλαπλεπζηηθφ.…”
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“…πλήζσο εκθαλίδεηαη ζε αζζελείο ειηθίαο κεγαιχηεξεο ησλ 18 ρξφλσλ κε FEV 1 κηθξφηεξε ηνπ 40% ηεο πξνβιεπφκελεο ηηκήο.Άιινη επηβαξπληηθνί παξάγνληεο είλαη ε παξνπζία P. aeruginosa, Burkholderia cepacia θαη εηδψλ Aspergillus89 . Ζ ζεξαπεία ηνπ πλεπκνζψξαθα ζηνρεχεη ηφζν ζηελ αζθαιή θαη απνηειεζκαηηθή ιχζε ηνπ, φζν θαη ζηελ πξφιεςε ππνηξνπήο ηνπ90 . Οη κηθξνί Οη παξαξξηλνθνιπίηηδεο απνηεινχλ ηηο ζπλεζέζηεξεο θιηληθέο εθδειψζεηο απφ ην αλψηεξν αλαπλεπζηηθφ.…”
unclassified