Síndrome de Mounier-Kühn

Fortuna, Fabrício Piccoli; Irion, Klaus; Wink, Cesare; Boemo, Jorge L.

doi:10.1590/s1806-37132006000200015

Cited by 23 publications

(6 citation statements)

References 4 publications

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“…Certain other conditions such as Marfan syndrome, Ehlers-Danlos syndrome, Kenny-Caffey syndrome, ataxia-telangiectasia, connective tissue diseases, Brachmann-de Lange syndrome, Bruton-type agammaglobulinemia, ankylosing spondylitis, cutis laxa, and light chain deposition disease are also associated with secondary tracheobronchial enlargement. [45]…”

Section: Discussionmentioning

confidence: 99%

A 46-year-old man with tracheomegaly, tracheal diverticulosis, and bronchiectasis: Mounier-Kuhn syndrome

et al. 2012

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Lower respiratory tract infection is one of the common causes of morbidity in India which is occasionally undiagnosed. In this regard tracheobronchomegaly is one of those conditions which masquerade as chronic bronchitis and bronchiectasis and are usually undiagnosed. It is a well-defined clinical and radiologic entity characterized by marked dilatation of the trachea and the central bronchi and is frequently associated with recurrent lower respiratory tract infection. Tracheobronchomegaly has been described by a variety of names, including Mounier-Kuhn syndrome, tracheal diverticulosis, tracheobronchiectasis, tracheocele, tracheomalacia, and tracheobronchopathia malacia.

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Section: Discussionmentioning

confidence: 99%

A 46-year-old man with tracheomegaly, tracheal diverticulosis, and bronchiectasis: Mounier-Kuhn syndrome

et al. 2012

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“…[1] The syndrome is characterized by marked tracheobronchial dilatation. [1–8] Most cases present in the third or later decades with recurrent respiratory tract infections. [6] Although the etiology is uncertain, it is believed to be due to the lack of smooth muscle and elastic connective tissue in the trachea and main bronchi, leading to sacculations and the formation of diverticula between the cartilaginous rings.…”

Section: Discussionmentioning

confidence: 99%

Case report: Mounier-Kuhn syndrome

Kachhawa

Meena

Jindal

et al. 2008

Indian Journal of Radiology and Imaging

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Tracheobronchomegaly or Mounier-Kuhn syndrome is a rare disorder characterized by marked dilatation of the trachea and main bronchi, bronchiectasis, and recurrent respiratory tract infections. The etiology of this disorder is uncertain and the clinical presentation is variable. The diagnosis is usually made on the basis of the characteristic CT scan findings. We report a case in a 21-year-old man presenting with recurrent lower respiratory tract infections.

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“…This leads to formation of diverticula and bronchiectasis and recurrent infections. The prevalence is relatively low, affecting between 1% and 4.5% of the population and generally presents in the third or fourth decade of life [4–7]. There is a strong male predominance (about 8:1) [6, 7] and most of the patients seem to be smokers.…”

Section: Discussionmentioning

confidence: 99%

An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome

Naciri¹,

Zahraoui²,

Soualhi³

et al. 2019

Case Reports in Pulmonology

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Mounier-Kuhn syndrome is a rare clinical and radiologic condition. It is characterized by tracheal and bronchial dilation. Diagnosis is made by computed tomography and bronchoscopy. An 81-year-old man presenting with an acute chest pain was referred to the pulmonology department. His chest computed tomographic scan showed a tracheobronchomegaly with an increase in the diameter of both the trachea and right and left main bronchi, associated with pneumomediastinum and fibrosis. Fiberoptic bronchoscopy revealed enlarged trachea and both main bronchi. These findings are consistent with a diagnosis of Mounier-Kuhn syndrome. Besides considering this long-neglected “orphan disease” when diagnosing spontaneous pneumomediastinum, clinicians should also be aware of an underlying Mounier-Kuhn syndrome in patients with recurrent respiratory infections, in order to avoid complications associated with the disease.

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Síndrome de Mounier-Kühn

Cited by 23 publications

References 4 publications

A 46-year-old man with tracheomegaly, tracheal diverticulosis, and bronchiectasis: Mounier-Kuhn syndrome

A 46-year-old man with tracheomegaly, tracheal diverticulosis, and bronchiectasis: Mounier-Kuhn syndrome

Case report: Mounier-Kuhn syndrome

An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome

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