Case for diagnosis

Abstract

A 27 year-old-man, with no known personal or familial history of disease, mentioned a 10-year history of asymptomatic groups of telangiectasias, with a Blaschko lines distribution on the right lateral aspect of the neck and asymptomatic. He denied any episodes of disease or drug intake that could be associated with the disease. Blood work had no changes, namely of liver enzymes or infectious serologies. The clinical diagnosis of Idiopathic Acquired Unilateral Nevoid Telangiectasia was made, an uncommon, benign vascular malformation. The patient declined doing a cutaneous biopsy or treatment with a cosmetic intent.

Capillary malformations: a classification using specific names for specific skin disorders

“…other hand, estrogen was often hold to be responsible, 106,110,111 whereas in other cases no initiating factor was discernible. 107,112,113 Unilateral naevoid telangiectasia of the patchy type Until today, unilateral naevoid telangiectasia of the patchy type is a poorly defined disorder. [114][115][116] It is included here for heuristic reasons.…”

Unilateral nevoid telangiectasia, diagnostic and therapeutic challenge

“…2 In order to define the possible cause of the condition, can carry out pregnancy tests, dosage of liver enzymes or serologies for hepatotrophic viruses. 6 The diagnosis of telangiectasia can be confirmed by histopathological examination, in which the presence of dilated and thin-walled capillaries in the papillary dermis, without endothelial proliferation or neoangiogenesis, mild perianexial and perivascular lymphocytic infiltrate. 2,6,9,13 However, it may require a perilesional skin biopsy for comparison.…”

“…The incidence of UNT is not known to be probably underreported. 6 Although it is a rare syndrome, the increase in reports in recent years suggests that UNT may be more common than previously. There is a predominance of this pathology in females in the proportion of 2:1.…”

“…2 From the third to fourth cervical dermatomes and the trigeminal nerve, face, shoulder, arm and upper trunk are the most involved sites, but the lower extremities (lumbar and sacral) may also be affected. 6,10 Some authors have observed that the metameric distribution usually follows the lines of Blaschko, this could be the result of the migration of cells during embryonic development. 2 Mazereeuw-Hautier et al reported an isolated case of pyogenic granuloma that developed on UNT affected skin.…”

“…The second one has a greater predilection for women during their fertile age and is linked to hyperestrogenism or elevation of vasoactive substances. 1,2,6…”