Mixoma de átrio direito com prolapso para o ventrículo direito

Abstract

We report on a rare case of a 67-year-old woman with a right atrial myxoma prolapsing into the right ventricle in the diastolic phase. These tumors comprise approximately 18% of all cardiac myxomas, which occur in 0.0017% of collected autopsy series. Descriptors: Myxoma. Heart neoplasms. Heart atria. Resumo Relatamos o caso raro de uma paciente de 67 anos, apresentando mixoma de átrio direito, com prolapso para o ventrículo direito. Estes tumores correspondem a cerca de 18% dos casos de mixoma, que por sua vez têm uma incidência de 0,0017% na população em geral. Descritores: Mixoma. Neoplasias cardíacas. Átrios do coração.

Mixoma auricular derecho en la infancia

“…Los mixomas de la aurícula derecha, en particular, pueden obstruir la válvula tricúspide, causando síntomas de insuficiencia cardíaca derecha, edema periférico, congestión hepática o muerte súbita, la cual ha sido reportada como más común entre los pacientes con mixomas auriculares derechos que protruyen a través de la válvula tricúspide, como es el caso de nuestro paciente 10,13 .…”

Right Ventricular Myxoma

“…Cardiac myxoma affects patients in the age range of 15 to 80 years, with an approximate average of 50 years, 2,4 slight female predominance (5:4) and, despite having a benign histological character, can lead to an adverse outcome, being responsible for incapacitating complications. 2,3,5 RV myxomas usually cause symptoms resulting from RVV obstruction, and symptoms of syncope, pulmonary embolism and sudden death may occur. 6,7 In the literature, there are few reports of isolated cases of RV myxomas, in most cases occurring with RVOT obstruction.…”

“…Imaging methods, particularly echocardiography, are the tests of choice for diagnosis, 7 with excellent sensitivity (95%) in detecting the tumor, which may reach 100% when associated with transesophageal echocardiography. 3,6 Schneider et al…”

“…They are preferentially located in the left atrium, with an incidence of 70 to 80%, 18% in the right atrium and, more rarely, from 2 to 5% in the ventricles, or multicentric. [3][4][5][6] Myxomas that originate in the right ventricle (RV) and obstruct the right ventricular outflow tract (RVOT) are extremely rare in children. 5 Patients present at least one of the characteristics of the classical triad described, which includes constitutional, embolic or obstructive symptoms.…”