2001
DOI: 10.1590/s0102-35862001000200009
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Síndrome de Jó ou hiperimunoglobulinemia E

Abstract: A síndrome de Jó ou hiperimunoglobulinemia E é uma rara condição de imunodeficiência, sem etiologia definida, caracterizada por infecções de repetição dos tratos respiratórios superior e inferior e da pele associadas a níveis elevados de imunoglobulina E, eosinofilia e alterações faciais peculiares. Relata-se o caso de um homem de 22 anos, portador da doença, complicada com empiema pleural e cistos pulmonares e boa evolução.

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(2 citation statements)
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“…1-5 This is an autosomal dominant disease, with sporadic cases detected, for which there is neither a predominant gender or race incidence. 1-5 …”
Section: Discussionmentioning
confidence: 99%
See 1 more Smart Citation
“…1-5 This is an autosomal dominant disease, with sporadic cases detected, for which there is neither a predominant gender or race incidence. 1-5 …”
Section: Discussionmentioning
confidence: 99%
“…1-6 Dermatoviroses, such as molluscum contagiosum and viral warts are common, mainly on areas with eczema. Those are difficult to treat, persisting for long periods of time.…”
Section: Discussionmentioning
confidence: 99%