Rabdomiomas cardíacos fetais: análise de cinco casos

Abstract

fetal morphological ultrasonography is the main form of early detection of primary cardiac tumors. The fetal cardiac evaluation is of fundamental importance for the differential morphological characterization of cardiac masses and for the evaluation of cardiac function. Rhabdomyomas are the most common type of fetal tumor. An expectant pre and postnatal conduct is followed, with a low risk of complications and with the possibility of spontaneous regression in most cases. Postnatal clinical follow-up is mandatory due to the high frequency of associated tuberous sclerosis.

Fetal cardiac tumors: prenatal diagnosis and outcomes

“…They may be intramural or intracavitary, and generally occupy the interventricular septum or right ventricle, close to the moderator band, but they can be located in any cardiac chamber [ 4 ] . Rhabdomyomas are hormone-dependent tumor, which explains their well-known capacity for spontaneous regression or reduction, along with their close relationship with tuberous sclerosis [ 5 ] . Fibromas rarely present during fetal life, but are generally located in the interventricular septum or the free wall of the left ventricle.…”

“…Rhabdomyomas can often impair the conduction system of the fetal heart and lead to heart rate disorders such as extrasystoles, supraventricular tachycardia or, less commonly, prolongation of the PR space, nonspecific alterations of ST follow-up, Wolf-Parkinson-White syndrome or aberrant atrioventricular conduction [ 1 , 5 , 7 , 10 ] . Wacker-Gussmann et al [ 1 ] evaluated the heart rate of 10 fetuses with rhabdomyoma, by means of electrophysiology, and observed that even the asymptomatic fetuses presented conduction disorders.…”