Traqueobroncomegalia (síndrome de Mounier-Kuhn): relato de caso e revisão da literatura

Abstract

A traqueobroncomegalia é uma rara entidade de etiologia incerta, caracterizada por dilatação marcante da traquéia e brônquios principais, bronquiectasias e infecções recorrentes do trato respiratório inferior. Sua apresentação clínica é inespecífica, sendo o diagnóstico realizado por métodos de imagem. Relata-se, neste trabalho, um caso de tal enfermidade, cujo diagnóstico confirmou-se por radiografia simples do tórax e por tomografia computadorizada. Unitermos: Traqueobroncomegalia. Síndrome de Mounier-Kuhn. Tomografia computadorizada. Tracheobronchomegaly (Mounier-Kuhn syndrome) -case report and review of the literature.Tracheobronchomegaly is a rare condition of uncertain etiology characterized by marked dilatation of the trachea and main bronchi, bronchiectasis and recurrent respiratory tract infections. Clinical presentation is nonspecific and the diagnosis is usually made by imaging methods. We report a case of a patient with tracheobronchomegaly. Diagnosis was confirmed by plain x-ray films and computed tomography of the chest.

Early manifestation of ARDS in COVID-19 infection in a 51- year-old man affected by Mounier-Kuhn syndrome

“…16 Similar radiological features were confirmed by Nobrega and Menon, with the diameter of trachea, right and left brochi being larger than 30 mm, 24 mm and 23 mm, respectively. 17,18 A remarkable trachea larger than 40 mm was reported by Bastos in a 33 year old man with MKS. 19 Likewise, Abdelghani described a 53 old man affected by MKS with a diameter of his trachea, right and left bronchi being of 50 mm, 38 mm and 34 mm respectively.…”

Síndrome de Mounier-Kuhn: achados radiológicos e apresentação clínica

“…fections, secretion accumulation and ineffective cough (1,2) . A subtle predominance of the disease is observed in men, at the third or fourth decades of life, but the exact prevalence is still to be determined, with very few cases reported in the literature (1-3) .…”