Anemia falciforme alterações angiográficas cerebrais

Abstract

Two cases of sickle cell disease with neurological complications are described. Cerebral angiograms were performed and a characteristic moyamoya-like angiographic pattern was demonstrated. This pattern results from a compensatory vascularization which may follow occlusion of the arteries at the base of the brain in several diseases. The risks of angiography and appropriate precautions are emphasized.

Moyamoya disease in Brazil

“…Although Yonekawa et al (2) and Goto & Yonekawa (3) have stated that five cases were described in Brazil, we found six reported cases with angiography suggestive of moyamoya disease (16)(17)(18)(19)(20). Nevertheless, the analysis of these cases shows that only two are true cases of moyamoya disease.…”

“…Garcia et al (17) described another case of moyamoya disease associated with two aneurysms of the basilar artery. The other four reported cases are more compatible with moyamoya syndrome since they are associated with Down syndrome (18), neurofibromatosis (19) and sickle-cell anemia in 2 patients (20).…”

Doença de moyamoya: Relato de caso e revisão da literatura brasileira

“…Revisando-se a literatura internacional, por meio do Medline e Lilacs, sobre esse assunto, encontrou-se 16 casos de DMM na população brasileira 1,3,[6][7][8]11,17 . Ressalta-se que o "fenômeno moyamoya" também tem sido descrito no Brasil por vários autores 2,10,14,24,27,31 .…”