\n,MD \s=b\Mature glial tissue was seen in the middle ear of a patient with no previous pathologic precedents, and a clinical diagnosis of serous otitis media was made. That anomaly was detected, and its corresponding clinical, roentgenographic, and pathologic findings are described. The results led us to diagnose it as a congenital (spontaneous) encephalocele of the middle ear. To our knowledge, other case of pure congenital encephalocele of the middle ear has been reported. (Arch Otolaryngol 1984;110:206-207) The major incidence of meningoencephaloceles (also called "brain fungus," "durai herniation," "brain hernia," "cerebral hernia," and "brain prolapse") takes place in the spinal column, especially at the lumbar and sacroiliac level (70% of the cases, according to Fisher et al1). In order of frequency, these are followed by the cervical and the occipitocervical regions.2 Within the ear, nose, and throat areas, this type of malforma¬ tion is seen with relative frequency at a nasal or nasosinusal level39; never¬ theless, its presence in the middle ear is rare.