Postural balance, handgrip strength and mobility in Brazilian children and adolescents with osteogenesis imperfecta

Functional status of individuals with osteogenesis imperfecta: data from a reference center

“…Multidimensional assessment with PEDI-CAT showed the studied sample performed below expectations in the mobility domain, with the worst results in OI type III. These findings also corroborate those of Coelho et al, 16 who also assessed the mobility of individuals with OI, through the mobility domain of the PEDI inventory, where type III participants had the worst result with a significant difference when compared to types I and IV. The assessment of mobility is of particular interest to the population with OI, as it is associated with various aspects of participation and quality of life.…”

“…It is noteworthy that only a small number of individuals in this sample were on physical therapy despite the fact most individuals were dependent on mobility or needed a wheelchair. In the sample evaluated by Coelho et al, 16 only 24% of the assessed children and adolescents reported performing some kind of physical activity.…”

“…Severe short stature was frequently found in the evaluated sample and composes a clinical characteristic of the disease that usually affects patients with OI type III or IV. 17 Coelho et al 16 , evaluated 50 Brazilian children and adolescents with OI, and found short stature in their sample, with a mean height (Z score) of -3.53 (± 2.59).…”

“…The findings here obtained to corroborate the results of a study by Brizola et al 19 When evaluating 62 children and adolescents with OI, they found that muscle strength assessed by manual muscle examination showed a difference when compared to type III to types I and IV for both upper and lower limb muscle strength. In a study by Coelho et al, 16 muscle strength was assessed using the handgrip and was found that the group with OI type III had significantly lower strength than OI types I and IV, and to the age-specific reference data.…”

Handgrip strength as a surrogate marker of lean mass and risk of malnutrition in paediatric patients

“…Likewise, the relationships between HGS with cardiovascular health, bone health, and total muscle mass have been studied in otherwise healthy children [ [9] , [10] , [11] ]. Previous research has also explored the use of HGS as a marker of muscle function in neurological and musculoskeletal disorders [ [12] , [13] , [14] , [15] ] and its relationship with muscle mass in chronic kidney disease and cystic fibrosis [ [16] , [17] , [18] ]. Whether HGS could be used as a screening method of malnutrition risk in sick children admitted to hospital has not yet been studied.…”