Marfan Syndrome: new diagnostic criteria, same anesthesia care? Case report and review

Abstract

Preoperative evaluation should focus on cardiopulmonary abnormalities. The anesthesiologist should be prepared for a potentially difficult intubation. Proper positioning and limb support prior to induction is crucial in order to avoid joint injuries. Consider antibiotic prophylaxis for subacute bacterial endocarditis. The patient should be carefully positioned to avoid joint injuries. Intraoperatively cardiovascular monitoring is mandatory: avoid maneuvers that can lead to tachycardia or hypertension, control airway pressure to prevent pneumothorax and maintain an adequate volemia to decrease chances of prolapse, especially if considering laparoscopic surgery. No single intraoperative anesthetic agent or technique has demonstrated superiority. Adequate postoperative pain management is vitally important to avoid the detrimental effects of hypertension and tachycardia.

Blunt Injury Forearm Debridement Under Ultrasound-Guided Regional Anesthesia for a Marfan Syndrome Patient

“…Our Marfan syndrome patient presented with a set of multiple cardiovascular complications which would be at very high risk when put under general anesthesia. Hence his forearm wound debridement surgery was then decided to be carried out by choosing ultrasound-guided in-plane supraclavicular brachial plexus nerve block [ 8 , 9 ].…”

Pectus excavatum como debut de síndrome de Marfan: reporte de caso

“…Fuente: Araújo, Marques, Freitas et al 7 El PE es una de las deformidades de la pared torácica más comunes, constituyendo el 88% del total de las mismas. Es importante recordar que el PE se encuentra incluido como un criterio mayor para el diagnóstico de SM 6 .…”

Iatrogenic injury to long thoracic nerve following thoracotomy for right thoracic scoliosis in Marfan syndrome: a case report

“…Marfan syndrome (MFS) is an illness of connective tissue, mainly involving the musculoskeletal, ocular, and cardiovascular systems [1], with an incidence of 2-3 per 10,000 population [1,2]. Scoliosis occurs in approximately 50-70% of patients with MFS and differs from idiopathic adolescent scoliosis with regard to curve pattern, progression, and symptoms [3].…”