Zebra-like dermatomyositis

Dupré, A

doi:10.1001/archderm.117.2.63a

Cited by 6 publications

(3 citation statements)

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“…Flagellate erythema‐associated amyopathic dermatomyositis has been described in 20% of cases, interstitial lung disease in 20% of cases, and concurrent malignancy was seen in 40% of cases . The one case of juvenile dermatomyositis with flagellate erythema that has been reported had clinical features similar to those of our case (e.g., nonpruritic linear streaks, heliotrope rash, Gottron papules, muscle involvement with high creatinine phosphokinase and transaminase levels) . Microscopic findings of flagellate erythema are nonspecific, with vacuolar degeneration of the basal layer and inflammatory infiltrate in the upper dermis.…”

Section: Discussionsupporting

confidence: 73%

Child with flagellate skin eruptions

Dhar

Srinivas

Dhar³

2018

Pediatric Dermatology

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Section: Discussionsupporting

confidence: 73%

Child with flagellate skin eruptions

Dhar

Srinivas

Dhar³

2018

Pediatric Dermatology

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“…The present case of Blaschko-linear dermatomyositis should not be confused with the flagellated linear skin lesions as sometimes found in patients with dermatomyositis [28, 29]. On the other hand, in cases of juvenile dermatomyositis a deep linear pattern of soft-tissue calcification, e.g.…”

Section: Discussionsupporting

confidence: 46%

Pronounced Linear Calcinosis in a Boy with Mild Dermatomyositis

et al. 2009

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A pronounced linear eruption with ulcerations and calcium extrusion present in a boy with a mild generalized rash clinically consistent with juvenile dermatomyositis or overlap syndrome is reported. Loss of heterozygosity (LOH) is a postzygotic mechanism by which a heterozygous somatic cell may become homozygous or hemizygous at a given gene locus. Such a mechanism can be suspected when a pronounced segmental manifestation of an acquired skin condition with a polygenic background is found to be superimposed on more or less symmetrically distributed nonsegmental lesions of the same disorder. Alternatively, such a segmental manifestation may reflect heterozygosity for a postzygotic mutation involving an additional gene locus. The severe linear lesions in our patient showed a Blaschko-linear arrangement and were superimposed on mild nonsegmental lesions of either amyopathic dermatomyositis or overlap syndrome. Either LOH or a postzygotic mutation at an additional gene locus may explain the pronounced linear involvement.

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“…Also, periungual telangiectasia, poikiloderma, subcutaneous calcinosis, panniculitis, mucinosis, and blister formation are occasionally or less frequently observed. In addition, linear violaceous, pruriginous lesions on the trunk have so‐called “linear streaks”, “zebra‐like stripe eruption”, “flagellate erythema” and “centripetal flagellate erythema” 45–50 . The typical feature of flagellate erythema associated with DM is shown in Fig.…”

Section: Dermatomyositis‐associated Flagellate Erythemamentioning

confidence: 99%