Unilateral Agenesis of Pulmonary Artery

Abstract

Isolated unilateral absence of pulmonary artery is uncommon. Although not certain, genetic, teratogenic and mechanical factors are held responsible. The anomaly results from the involution of the proximal sixth aortic arch. In this report we present an asymptomatic 24 yrs old male patient. Unilateral right-sided absence of pulmonary artery was diagnosed by thoracic computerized tomography (CT) and angiographic evaluation.

Incidental finding in a newborn with respiratory distress

“…Unilateral absence of the pulmonary artery is a rare congenital lesion with an estimated prevalence of 1/200,000. ( 1 ) It is generally associated with other cardiovascular anomalies, although isolated form may also occur. ( 2 ) The latter is rarely diagnosed during the neonatal period.…”