Tessier 30 Facial Cleft- Median Cleft of Upper and Lower Lip, Lower Alveolus and Mandible, Ankyloglossia and Cervical Teratoma

Abstract

Tessier cleft no. 30 is a rare congenital anomaly. It may range in severity from median cleft of the upper and lower lip to cleft of the manubrium sterni involving the mandible, floor of the mouth, tongue, hyoid bone, thyroid cartilage and strap muscles. Ankyloglossia and median web in the neck extending from chin resulting in neck contracture are frequently found. This is a case report of median cleft of upper and lower lip, lower alveolus, mandible with severe ankyloglossia, a fibrotic band extending from the chin to the suprasternal notch and cervical teratoma; in a new born female. The deformity was corrected as staged procedure i.e. removal of cervical teratoma, release of the tongue from floor of the mouth and lower alveolus, repair of the cleft lower lip, excision of the fibrotic band and correction of neck contracture with multiple Z-plasties. Fixation of the mandibular cleft, orthodontic treatment of upper teeth, rhinoplasty and otoplasty will be done by surgeries in future.

Tessier 30 Facial Cleft: A Rare Craniofacial Anomaly

“…The severity of the cleft increases if a defect occurs in the early embryonic period, that is, interference in the development of neural crest cells along the fusion planes during the early formative stages of the facial skeleton. 3 …”