Takayasu's Arteritis Presenting as Pulmonary Hypertension

Predictors for pulmonary artery involvement in Takayasu arteritis and its cluster analysis

“…In another study from Korea evaluating CT angiography of 10 TAK patients [ 15 ], the three patients who had PAI [ 22 ] were among those diagnosed with the involvement of aortic arch and its branches. In other case studies, PAI has also been reported to be accompanied with wall thickening of the thoracic aorta [ 8 , 16 – 19 ], dilation or narrowing of the ascending aorta [ 20 ], and slightly prominent thoracic aorta [ 21 ]. Thus, the involvement of the thoracic aorta can be used as a predictor of PAI in TAK patients.…”

Imaging Features of Takayasu Disease

“…In the second pattern, pulmonary artery stenoses may be distal, isolated, or associated with proximal lesions. Finally, pulmonary arteriolitis without involvement of the large arteries has been described (Haas and Stiehm 1986).…”

Open Lung Biopsy in Primary Pulmonary Hypertension: A Decision Analysis

“…10 Occasionally, patients with PPH may prove to have radiologically inapparent fibrotic lung disease 1 or sarcoidosis 11,12 with minor reduction in lung volumes. Sporadic cases of intravascular lesions from Takayasu's arteritis, [13][14][15] mixed connective tissue disease, 16,17 systemic lupus, [18][19][20] rheumatoid disease, 21 scleroderma, 22 sarcoidosis, 23 and foreign body vasculitis 24,25 26 and could be missed on routine testing.…”